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Craniometaphyseal dysplasia: Report of 2 cases with an emphasis on panoramic imaging features
Craniometaphyseal dysplasia (CMD) is a rare hereditary disorder characterized by hyperostosis of the craniofacial bones and flared metaphyses of the long bones. Although some reports have described the dentomaxillofacial characteristics of CMD, including increased density of the jaw, malocclusion, a...
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Korean Academy of Oral and Maxillofacial Radiology
2018
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6305782/ https://www.ncbi.nlm.nih.gov/pubmed/30607353 http://dx.doi.org/10.5624/isd.2018.48.4.283 |
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author | Yeom, Han-Gyeol |
author_facet | Yeom, Han-Gyeol |
author_sort | Yeom, Han-Gyeol |
collection | PubMed |
description | Craniometaphyseal dysplasia (CMD) is a rare hereditary disorder characterized by hyperostosis of the craniofacial bones and flared metaphyses of the long bones. Although some reports have described the dentomaxillofacial characteristics of CMD, including increased density of the jaw, malocclusion, and delayed eruption of the permanent teeth, only a few studies have reported the distinct imaging features of CMD on panoramic radiography. This report presents 2 cases of confirmed CMD patients with an emphasis on panoramic imaging features. The patients' images revealed hyperostosis and sclerosis of the maxilla and mandibular alveolar bone, but there was no change in the mandibular basal bone. In both cases, the mandibular condyle heads exhibited a short clubbed shape with hyperplasia of the coronoid process. For patients without clear otorhinolaryngological symptoms, common radiologic features of CMD could be visualized by routinely-taken panoramic radiographs, and further medical examinations and treatment can be recommended. |
format | Online Article Text |
id | pubmed-6305782 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | Korean Academy of Oral and Maxillofacial Radiology |
record_format | MEDLINE/PubMed |
spelling | pubmed-63057822019-01-03 Craniometaphyseal dysplasia: Report of 2 cases with an emphasis on panoramic imaging features Yeom, Han-Gyeol Imaging Sci Dent Case Report Craniometaphyseal dysplasia (CMD) is a rare hereditary disorder characterized by hyperostosis of the craniofacial bones and flared metaphyses of the long bones. Although some reports have described the dentomaxillofacial characteristics of CMD, including increased density of the jaw, malocclusion, and delayed eruption of the permanent teeth, only a few studies have reported the distinct imaging features of CMD on panoramic radiography. This report presents 2 cases of confirmed CMD patients with an emphasis on panoramic imaging features. The patients' images revealed hyperostosis and sclerosis of the maxilla and mandibular alveolar bone, but there was no change in the mandibular basal bone. In both cases, the mandibular condyle heads exhibited a short clubbed shape with hyperplasia of the coronoid process. For patients without clear otorhinolaryngological symptoms, common radiologic features of CMD could be visualized by routinely-taken panoramic radiographs, and further medical examinations and treatment can be recommended. Korean Academy of Oral and Maxillofacial Radiology 2018-12 2018-12-20 /pmc/articles/PMC6305782/ /pubmed/30607353 http://dx.doi.org/10.5624/isd.2018.48.4.283 Text en Copyright © 2018 by Korean Academy of Oral and Maxillofacial Radiology http://creativecommons.org/licenses/by-nc/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Yeom, Han-Gyeol Craniometaphyseal dysplasia: Report of 2 cases with an emphasis on panoramic imaging features |
title | Craniometaphyseal dysplasia: Report of 2 cases with an emphasis on panoramic imaging features |
title_full | Craniometaphyseal dysplasia: Report of 2 cases with an emphasis on panoramic imaging features |
title_fullStr | Craniometaphyseal dysplasia: Report of 2 cases with an emphasis on panoramic imaging features |
title_full_unstemmed | Craniometaphyseal dysplasia: Report of 2 cases with an emphasis on panoramic imaging features |
title_short | Craniometaphyseal dysplasia: Report of 2 cases with an emphasis on panoramic imaging features |
title_sort | craniometaphyseal dysplasia: report of 2 cases with an emphasis on panoramic imaging features |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6305782/ https://www.ncbi.nlm.nih.gov/pubmed/30607353 http://dx.doi.org/10.5624/isd.2018.48.4.283 |
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