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Acquired Localized Cutis Laxa: A Case Report and the Role of Plastic Surgery

Cutis laxa is an uncommon connective tissue disorder affecting the elastin fibers leading to lax and pendulous skin and in generalized form can present with systemic involvement. Congenital cutis laxa is common in comparison to acquired cutis laxa and has varied inheritance patterns. Treatment is ch...

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Detalles Bibliográficos
Autores principales: Reddy, Guru Prasad, Mishra, Brijesh, Upadhyaya, Divya Narain
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6340237/
https://www.ncbi.nlm.nih.gov/pubmed/30745636
http://dx.doi.org/10.4103/ijd.IJD_14_18
Descripción
Sumario:Cutis laxa is an uncommon connective tissue disorder affecting the elastin fibers leading to lax and pendulous skin and in generalized form can present with systemic involvement. Congenital cutis laxa is common in comparison to acquired cutis laxa and has varied inheritance patterns. Treatment is chiefly observation in congenital cutis laxa, and there is a paucity of literature on surgical management in acquired cutis laxa. We report a rare case of acquired localized cutis laxa with a review of literature on the role of plastic surgery in this condition.