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Unroofed coronary sinus: An unusual interatrial communication and a rare childhood entity

Unroofed coronary sinus, an unusual form of interatrial communication, is a rare cardiac anomaly. It is not a true defect of the atrial septum. It is described as a partial (focal or fenestrated) or complete absence of the roof of the coronary sinus, resulting in a communication between the coronary...

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Autores principales: Murli, Lakshmi, Ranjit, M S, Shah, Prashant
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6343380/
https://www.ncbi.nlm.nih.gov/pubmed/30745774
http://dx.doi.org/10.4103/apc.APC_119_18
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author Murli, Lakshmi
Ranjit, M S
Shah, Prashant
author_facet Murli, Lakshmi
Ranjit, M S
Shah, Prashant
author_sort Murli, Lakshmi
collection PubMed
description Unroofed coronary sinus, an unusual form of interatrial communication, is a rare cardiac anomaly. It is not a true defect of the atrial septum. It is described as a partial (focal or fenestrated) or complete absence of the roof of the coronary sinus, resulting in a communication between the coronary sinus and left atrium. It is presumably the least common variety of defects associated with interatrial shunting. Such defects are often difficult to diagnose and may even be overlooked during surgery for complex congenital heart disease. In most cases, they are associated with a persistent left superior vena cava, pulmonary or tricuspid atresia, and hearts with isomeric right atrial appendages. We report a case of this unusual form of interatrial communication without any associated anomalies in a 7-year-old girl child who presented to us with exertional dyspnea.
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spelling pubmed-63433802019-02-11 Unroofed coronary sinus: An unusual interatrial communication and a rare childhood entity Murli, Lakshmi Ranjit, M S Shah, Prashant Ann Pediatr Cardiol Case Report Unroofed coronary sinus, an unusual form of interatrial communication, is a rare cardiac anomaly. It is not a true defect of the atrial septum. It is described as a partial (focal or fenestrated) or complete absence of the roof of the coronary sinus, resulting in a communication between the coronary sinus and left atrium. It is presumably the least common variety of defects associated with interatrial shunting. Such defects are often difficult to diagnose and may even be overlooked during surgery for complex congenital heart disease. In most cases, they are associated with a persistent left superior vena cava, pulmonary or tricuspid atresia, and hearts with isomeric right atrial appendages. We report a case of this unusual form of interatrial communication without any associated anomalies in a 7-year-old girl child who presented to us with exertional dyspnea. Medknow Publications & Media Pvt Ltd 2019 /pmc/articles/PMC6343380/ /pubmed/30745774 http://dx.doi.org/10.4103/apc.APC_119_18 Text en Copyright: © 2019 Annals of Pediatric Cardiology http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Murli, Lakshmi
Ranjit, M S
Shah, Prashant
Unroofed coronary sinus: An unusual interatrial communication and a rare childhood entity
title Unroofed coronary sinus: An unusual interatrial communication and a rare childhood entity
title_full Unroofed coronary sinus: An unusual interatrial communication and a rare childhood entity
title_fullStr Unroofed coronary sinus: An unusual interatrial communication and a rare childhood entity
title_full_unstemmed Unroofed coronary sinus: An unusual interatrial communication and a rare childhood entity
title_short Unroofed coronary sinus: An unusual interatrial communication and a rare childhood entity
title_sort unroofed coronary sinus: an unusual interatrial communication and a rare childhood entity
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6343380/
https://www.ncbi.nlm.nih.gov/pubmed/30745774
http://dx.doi.org/10.4103/apc.APC_119_18
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