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Tuberous sclerosis complex exhibits a new renal cystogenic mechanism

Tuberous sclerosis complex (TSC) is a tumor predisposition syndrome with significant renal cystic and solid tumor disease. While the most common renal tumor in TSC, the angiomyolipoma, exhibits a loss of heterozygosity associated with disease, we have discovered that the renal cystic epithelium is c...

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Detalles Bibliográficos
Autores principales:	Bissler, John J., Zadjali, Fahad, Bridges, Dave, Astrinidis, Aristotelis, Barone, Sharon, Yao, Ying, Redd, JeAnna R., Siroky, Brian J., Wang, Yanqing, Finley, Joel T., Rusiniak, Michael E., Baumann, Heinz, Zahedi, Kamyar, Gross, Kenneth W., Soleimani, Manoocher
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley and Sons Inc. 2019
Materias:	Original Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6344348/ https://www.ncbi.nlm.nih.gov/pubmed/30675765 http://dx.doi.org/10.14814/phy2.13983

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