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Molecular Mechanisms of Neurodegeneration Related to C9orf72 Hexanucleotide Repeat Expansion

Two clinically distinct diseases, amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD), have recently been classified as two extremes of the FTD/ALS spectrum. The neuropathological correlate of FTD is frontotemporal lobar degeneration (FTLD), characterized by tau-, TDP-43-, and FUS-...

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Detalles Bibliográficos
Autores principales:	Babić Leko, Mirjana, Župunski, Vera, Kirincich, Jason, Smilović, Dinko, Hortobágyi, Tibor, Hof, Patrick R., Šimić, Goran
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Hindawi 2019
Materias:	Review Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6350563/ https://www.ncbi.nlm.nih.gov/pubmed/30774737 http://dx.doi.org/10.1155/2019/2909168

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