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Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy

Creutzfeldt–Jakob disease (CJD) presents with seizures as an early symptom in only approximately 3% of cases. These seizures often present as nonconvulsive status epilepticus (NCSE) or epilepsia partialis continua (EPC). Here, we describe a case of probable sporadic CJD (sCJD) in an 83-year-old man...

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Detalles Bibliográficos
Autores principales: Hsiao, Pei-Shan, Lee, Yuan-Ming, Chu, Fu-Sin, Lee, Chao-Lin, Liu, Fang-Chun, Tsai, Ping-Huang
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6369248/
https://www.ncbi.nlm.nih.gov/pubmed/30788213
http://dx.doi.org/10.1016/j.ebcr.2019.01.006
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author Hsiao, Pei-Shan
Lee, Yuan-Ming
Chu, Fu-Sin
Lee, Chao-Lin
Liu, Fang-Chun
Tsai, Ping-Huang
author_facet Hsiao, Pei-Shan
Lee, Yuan-Ming
Chu, Fu-Sin
Lee, Chao-Lin
Liu, Fang-Chun
Tsai, Ping-Huang
author_sort Hsiao, Pei-Shan
collection PubMed
description Creutzfeldt–Jakob disease (CJD) presents with seizures as an early symptom in only approximately 3% of cases. These seizures often present as nonconvulsive status epilepticus (NCSE) or epilepsia partialis continua (EPC). Here, we describe a case of probable sporadic CJD (sCJD) in an 83-year-old man whose manifest an unusual presentation of left-hand tonic seizures without evolution to EPC, as well as brain MRI findings interpreted as peri-ictal changes, which led to an initial misdiagnosis of focal epilepsy.
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spelling pubmed-63692482019-02-20 Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy Hsiao, Pei-Shan Lee, Yuan-Ming Chu, Fu-Sin Lee, Chao-Lin Liu, Fang-Chun Tsai, Ping-Huang Epilepsy Behav Case Rep Article Creutzfeldt–Jakob disease (CJD) presents with seizures as an early symptom in only approximately 3% of cases. These seizures often present as nonconvulsive status epilepticus (NCSE) or epilepsia partialis continua (EPC). Here, we describe a case of probable sporadic CJD (sCJD) in an 83-year-old man whose manifest an unusual presentation of left-hand tonic seizures without evolution to EPC, as well as brain MRI findings interpreted as peri-ictal changes, which led to an initial misdiagnosis of focal epilepsy. Elsevier 2019-01-26 /pmc/articles/PMC6369248/ /pubmed/30788213 http://dx.doi.org/10.1016/j.ebcr.2019.01.006 Text en © 2019 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Article
Hsiao, Pei-Shan
Lee, Yuan-Ming
Chu, Fu-Sin
Lee, Chao-Lin
Liu, Fang-Chun
Tsai, Ping-Huang
Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title_full Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title_fullStr Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title_full_unstemmed Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title_short Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title_sort probable sporadic creutzfeldt–jakob disease mimicking focal epilepsy
topic Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6369248/
https://www.ncbi.nlm.nih.gov/pubmed/30788213
http://dx.doi.org/10.1016/j.ebcr.2019.01.006
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