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Spontaneous regression of a sporadic intra-abdominal located desmoid-type fibromatosis
BACKGROUND: Desmoid-type fibromatosis (DTF) is a rare benign proliferation of myofibroblasts with an unpredictable disease course. Treatment of intra-abdominal located DTF is difficult because of the close relationship with vital organs. CASE PRESENTATION: A healthy young male presents with an asymp...
Autores principales: | , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6371851/ https://www.ncbi.nlm.nih.gov/pubmed/30792846 http://dx.doi.org/10.1093/jscr/rjz037 |
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author | Kloeze, Jurian van Veen, Martin |
author_facet | Kloeze, Jurian van Veen, Martin |
author_sort | Kloeze, Jurian |
collection | PubMed |
description | BACKGROUND: Desmoid-type fibromatosis (DTF) is a rare benign proliferation of myofibroblasts with an unpredictable disease course. Treatment of intra-abdominal located DTF is difficult because of the close relationship with vital organs. CASE PRESENTATION: A healthy young male presents with an asymptomatic palpable mass in the lower right abdominal quadrant. A computed tomography shows a 10 × 7 cm(2) pear-shaped mass, and pathological examination revealed DTF. A watchful waiting approach was initiated, as the patient was asymptomatic and surgery would imply a significant amount of intestinal resection. After a follow-up of 2 years, the tumor has regressed spontaneously and the patient is still without symptoms. CONCLUSIONS: DTF is a difficult to treat condition where individualized management is appropriate. An asymptomatic patient could be treated with a watchful waiting approach, even with intra-abdominal location. Thereby sparing unnecessary morbidity as the tumor can be stable for many years or even regress spontaneously. |
format | Online Article Text |
id | pubmed-6371851 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2019 |
publisher | Oxford University Press |
record_format | MEDLINE/PubMed |
spelling | pubmed-63718512019-02-21 Spontaneous regression of a sporadic intra-abdominal located desmoid-type fibromatosis Kloeze, Jurian van Veen, Martin J Surg Case Rep Case Report BACKGROUND: Desmoid-type fibromatosis (DTF) is a rare benign proliferation of myofibroblasts with an unpredictable disease course. Treatment of intra-abdominal located DTF is difficult because of the close relationship with vital organs. CASE PRESENTATION: A healthy young male presents with an asymptomatic palpable mass in the lower right abdominal quadrant. A computed tomography shows a 10 × 7 cm(2) pear-shaped mass, and pathological examination revealed DTF. A watchful waiting approach was initiated, as the patient was asymptomatic and surgery would imply a significant amount of intestinal resection. After a follow-up of 2 years, the tumor has regressed spontaneously and the patient is still without symptoms. CONCLUSIONS: DTF is a difficult to treat condition where individualized management is appropriate. An asymptomatic patient could be treated with a watchful waiting approach, even with intra-abdominal location. Thereby sparing unnecessary morbidity as the tumor can be stable for many years or even regress spontaneously. Oxford University Press 2019-02-12 /pmc/articles/PMC6371851/ /pubmed/30792846 http://dx.doi.org/10.1093/jscr/rjz037 Text en Published by Oxford University Press and JSCR Publishing Ltd. All rights reserved. © The Author(s) 2019. http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com |
spellingShingle | Case Report Kloeze, Jurian van Veen, Martin Spontaneous regression of a sporadic intra-abdominal located desmoid-type fibromatosis |
title | Spontaneous regression of a sporadic intra-abdominal located desmoid-type fibromatosis |
title_full | Spontaneous regression of a sporadic intra-abdominal located desmoid-type fibromatosis |
title_fullStr | Spontaneous regression of a sporadic intra-abdominal located desmoid-type fibromatosis |
title_full_unstemmed | Spontaneous regression of a sporadic intra-abdominal located desmoid-type fibromatosis |
title_short | Spontaneous regression of a sporadic intra-abdominal located desmoid-type fibromatosis |
title_sort | spontaneous regression of a sporadic intra-abdominal located desmoid-type fibromatosis |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6371851/ https://www.ncbi.nlm.nih.gov/pubmed/30792846 http://dx.doi.org/10.1093/jscr/rjz037 |
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