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Glycomacropeptide: long-term use and impact on blood phenylalanine, growth and nutritional status in children with PKU

ABSTRACT: In phenylketonuria, casein glycomacropeptide (CGMP) requires modification with the addition of some essential and semi essential amino acids to ensure suitability as a protein substitute. The optimal amount and ratio of additional amino acids is undefined. AIM: A longitudinal, parallel, co...

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Detalles Bibliográficos
Autores principales:	Daly, A., Evans, S., Chahal, S., Santra, S., Pinto, A., Jackson, R., Gingell, C., Rocha, J., Van Spronsen, F. J., MacDonald, A.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2019
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6377744/ https://www.ncbi.nlm.nih.gov/pubmed/30770754 http://dx.doi.org/10.1186/s13023-019-1011-y

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