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The Role of Iron in Friedreich’s Ataxia: Insights From Studies in Human Tissues and Cellular and Animal Models
Friedreich’s ataxia (FRDA) is a rare early-onset degenerative disease that affects both the central and peripheral nervous systems, and other extraneural tissues, mainly the heart and endocrine pancreas. This disorder progresses as a mixed sensory and cerebellar ataxia, primarily disturbing the prop...
Autores principales: | Llorens, José Vicente, Soriano, Sirena, Calap-Quintana, Pablo, Gonzalez-Cabo, Pilar, Moltó, María Dolores |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6387962/ https://www.ncbi.nlm.nih.gov/pubmed/30833885 http://dx.doi.org/10.3389/fnins.2019.00075 |
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