Cargando…

Regional lung densities in alpha-1 antitrypsin deficiency compared to predicted values

BACKGROUND: We developed a method to calculate a standard score for lung tissue mass derived from CT scan images from a control group without respiratory disease. We applied the method to images from subjects with emphysema associated with alpha-1 antitrypsin deficiency (AATD) and used it to study r...

Descripción completa

Detalles Bibliográficos
Autores principales:	Stoel, Berend C., Stolk, Jan, Bakker, M. Els, Parr, David G.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2019
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6396535/ https://www.ncbi.nlm.nih.gov/pubmed/30819163 http://dx.doi.org/10.1186/s12931-019-1012-3

Ejemplares similares

Therapeutic efficacy of alpha-1 antitrypsin augmentation therapy on the loss of lung tissue: an integrated analysis of 2 randomised clinical trials using computed tomography densitometry
por: Stockley, Robert A, et al.
Publicado: (2010)

Detection of emphysema progression in alpha 1-antitrypsin deficiency using CT densitometry; Methodological advances
por: Parr, David G, et al.
Publicado: (2008)

Lung function and CT lung densitometry in 37- to 39-year-old individuals with alpha-1-antitrypsin deficiency
por: Mostafavi, Behrouz, et al.
Publicado: (2018)

The Relationship between Plasma Alpha-1-Antitrypsin Polymers and Lung or Liver Function in ZZ Alpha-1-Antitrypsin-Deficient Patients
por: Sark, Annelot D., et al.
Publicado: (2022)

Hereditary alpha-1-antitrypsin deficiency and its clinical consequences
por: Fregonese, Laura, et al.
Publicado: (2008)

Alpha(1)-antitrypsin deficiency: current perspective on research, diagnosis, and management
por: Stolk, Jan, et al.
Publicado: (2006)

Prediction of lung function and lung density of young adults who had bronchopulmonary dysplasia
por: Santema, Helger Y., et al.
Publicado: (2020)

Predicting Lung Function Using Biomarkers in Alpha-1 Antitrypsin Deficiency
por: Spittle, Daniella A., et al.
Publicado: (2023)

alpha 1-Antitrypsin deficiency and susceptibility to lung disease.
por: Evans, H E, et al.
Publicado: (1979)

Alpha 1 antitrypsin to treat lung disease in alpha 1 antitrypsin deficiency: recent developments and clinical implications
por: Chapman, Kenneth R, et al.
Publicado: (2018)

Clinical and functional characteristics of individuals with alpha-1 antitrypsin deficiency: EARCO international registry
por: Miravitlles, Marc, et al.
Publicado: (2022)

Mineralization of alpha-1-antitrypsin inclusion bodies in Mmalton alpha-1-antitrypsin deficiency
por: Callea, Francesco, et al.
Publicado: (2018)

Lung and liver transplantation in patients with alpha-1 antitrypsin deficiency
por: Zamora, Martin R., et al.
Publicado: (2021)

Correction: Clinical and functional characteristics of individuals with alpha-1 antitrypsin deficiency: EARCO international registry
por: Miravitlles, Marc, et al.
Publicado: (2023)

Gene therapy for alpha 1-antitrypsin deficiency with an oxidant-resistant human alpha 1-antitrypsin
por: Sosulski, Meredith L., et al.
Publicado: (2020)

Alpha-1 Antitrypsin as a Therapeutic Agent for Conditions not Associated with Alpha-1 Antitrypsin Deficiency
por: Wanner, Adam
Publicado: (2015)

The effect of exacerbations on lung density in α(1)-antitrypsin deficiency
por: Strange, Charlie, et al.
Publicado: (2023)

Protease-Specific Biomarkers to Analyse Protease Inhibitors for Emphysema Associated with Alpha 1-Antitrypsin Deficiency. An Overview of Current Approaches
por: Viglio, Simona, et al.
Publicado: (2021)

Lung Inflammation in alpha-1-antitrypsin deficient individuals with normal lung function
por: Kokturk, Nurdan, et al.
Publicado: (2023)

Alpha-1 antitrypsin deficiency impairs lung antibacterial immunity in mice
por: Ostermann, Lena, et al.
Publicado: (2021)

Safety and efficacy of alpha-1-antitrypsin augmentation therapy in the treatment of patients with alpha-1-antitrypsin deficiency
por: Petrache, Irina, et al.
Publicado: (2009)

A comparative ultrastructural and molecular biological study on Chlamydia psittaci infection in alpha-1 antitrypsin deficiency and non-alpha-1 antitrypsin deficiency emphysema versus lung tissue of patients with hamartochondroma
por: Theegarten, Dirk, et al.
Publicado: (2004)

alpha1-Antitrypsin deficiency and hepatocellular cancer.
por: Kew, M. C., et al.
Publicado: (1978)

The prevalence of alpha-1 antitrypsin deficiency in Ireland
por: Carroll, Tomás P, et al.
Publicado: (2011)

Alpha-1 Antitrypsin Deficiency: The Learning Goes On
por: Stockley, Robert. A.
Publicado: (2020)

Monocytes and Macrophages in Alpha-1 Antitrypsin Deficiency
por: Belchamber, Kylie B R, et al.
Publicado: (2020)

Alpha-1 Antitrypsin Deficiency: Home Therapy
por: Annunziata, Anna, et al.
Publicado: (2021)

Clinical utility of alpha-1 proteinase inhibitor in the management of adult patients with severe alpha-1 antitrypsin deficiency: a review of the current literature
por: Parr, David G, et al.
Publicado: (2017)

Bronchoscopic Lung Volume Reduction in Patients with Emphysema due to Alpha-1 Antitrypsin Deficiency
por: Everaerts, Stephanie, et al.
Publicado: (2023)

Methods of Purification and Application Procedures of Alpha1 Antitrypsin: A Long-Lasting History
por: Viglio, Simona, et al.
Publicado: (2020)

Structural characterization and conformational dynamics of alpha-1 antitrypsin pathogenic variants causing alpha-1-antitrypsin deficiency
por: Shaik, Noor Ahmad, et al.
Publicado: (2022)

Survival in severe alpha-1-antitrypsin deficiency (PiZZ)
por: Tanash, Hanan A, et al.
Publicado: (2010)

The Role of Computed Tomography for the Evaluation of Lung Disease in Alpha-1 Antitrypsin Deficiency
por: Campos, Michael A., et al.
Publicado: (2018)

Treatment of lung disease in alpha-1 antitrypsin deficiency: a systematic review
por: Edgar, Ross G, et al.
Publicado: (2017)

Alpha-1 antitrypsin deficiency and risk of lung cancer: A systematic review
por: Tubío-Pérez, Ramón A., et al.
Publicado: (2020)

Ferret models of alpha-1 antitrypsin deficiency develop lung and liver disease
por: He, Nan, et al.
Publicado: (2022)

Short-term variability of biomarkers of proteinase activity in patients with emphysema associated with type Z alpha-1-antitrypsin deficiency
por: Stolk, Jan, et al.
Publicado: (2005)

Alpha 1 Antitrypsin Deficiency in Infants with Neonatal Cholestasis
por: Monajemzadeh, Maryam, et al.
Publicado: (2013)

Cardiovascular risk in patients with alpha-1-antitrypsin deficiency
por: Fähndrich, Sebastian, et al.
Publicado: (2017)

The Importance of Early Identification of Alpha-1 Antitrypsin Deficiency
por: Buttar, Barjinder S, et al.
Publicado: (2018)

Cannot write session to /tmp/vufind_sessions/sess_e74su6nmt00i3elkjg107ndavd