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Angioedema due to acquired C1-inhibitor deficiency: spectrum and treatment with C1-inhibitor concentrate

BACKGROUND: Acquired angioedema due to C1-inhibitor (C1-INH) deficiency (AAE-C1-INH) is a serious condition that may result in life-threatening asphyxiation due to laryngeal edema. It is associated with malignant B-cell lymphoma and other disorders. The purpose of this study was to describe the char...

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Detalles Bibliográficos
Autores principales:	Bork, Konrad, Staubach-Renz, Petra, Hardt, Jochen
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2019
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6417199/ https://www.ncbi.nlm.nih.gov/pubmed/30866985 http://dx.doi.org/10.1186/s13023-019-1043-3

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