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Phosphaturic Mesenchymal Tumors Involving Skull Bones: Report of Two Rare Cases

Phosphaturic mesenchymal tumor (PMT) is a rare tumor causing oncogenic osteomalacia (OO). Most such tumors occur in soft tissue and bones of extremities and appendicular skeleton. Intracranial location and involvement of temporal–occipital bone is extremely rare. We report two unusual cases: The fir...

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Autores principales: Mishra, Toshi, Desouza, Maria Alina, Patel, Keyuri, Mazumdar, Girish A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6417335/
https://www.ncbi.nlm.nih.gov/pubmed/30937047
http://dx.doi.org/10.4103/ajns.AJNS_176_17
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author Mishra, Toshi
Desouza, Maria Alina
Patel, Keyuri
Mazumdar, Girish A.
author_facet Mishra, Toshi
Desouza, Maria Alina
Patel, Keyuri
Mazumdar, Girish A.
author_sort Mishra, Toshi
collection PubMed
description Phosphaturic mesenchymal tumor (PMT) is a rare tumor causing oncogenic osteomalacia (OO). Most such tumors occur in soft tissue and bones of extremities and appendicular skeleton. Intracranial location and involvement of temporal–occipital bone is extremely rare. We report two unusual cases: The first was intracranial, involving the temporal bone, while the other was a skull base tumor arising from the occipital–temporal bone. Both of them presented with paraneoplastic syndrome of OO, resembled a meningioma radiologically, and underwent gross total resection of tumor. Histologically, both of them were diagnosed as PMT, mixed connective tissue variant.
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spelling pubmed-64173352019-04-01 Phosphaturic Mesenchymal Tumors Involving Skull Bones: Report of Two Rare Cases Mishra, Toshi Desouza, Maria Alina Patel, Keyuri Mazumdar, Girish A. Asian J Neurosurg Case Report Phosphaturic mesenchymal tumor (PMT) is a rare tumor causing oncogenic osteomalacia (OO). Most such tumors occur in soft tissue and bones of extremities and appendicular skeleton. Intracranial location and involvement of temporal–occipital bone is extremely rare. We report two unusual cases: The first was intracranial, involving the temporal bone, while the other was a skull base tumor arising from the occipital–temporal bone. Both of them presented with paraneoplastic syndrome of OO, resembled a meningioma radiologically, and underwent gross total resection of tumor. Histologically, both of them were diagnosed as PMT, mixed connective tissue variant. Medknow Publications & Media Pvt Ltd 2019 /pmc/articles/PMC6417335/ /pubmed/30937047 http://dx.doi.org/10.4103/ajns.AJNS_176_17 Text en Copyright: © 2018 Asian Journal of Neurosurgery http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Mishra, Toshi
Desouza, Maria Alina
Patel, Keyuri
Mazumdar, Girish A.
Phosphaturic Mesenchymal Tumors Involving Skull Bones: Report of Two Rare Cases
title Phosphaturic Mesenchymal Tumors Involving Skull Bones: Report of Two Rare Cases
title_full Phosphaturic Mesenchymal Tumors Involving Skull Bones: Report of Two Rare Cases
title_fullStr Phosphaturic Mesenchymal Tumors Involving Skull Bones: Report of Two Rare Cases
title_full_unstemmed Phosphaturic Mesenchymal Tumors Involving Skull Bones: Report of Two Rare Cases
title_short Phosphaturic Mesenchymal Tumors Involving Skull Bones: Report of Two Rare Cases
title_sort phosphaturic mesenchymal tumors involving skull bones: report of two rare cases
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6417335/
https://www.ncbi.nlm.nih.gov/pubmed/30937047
http://dx.doi.org/10.4103/ajns.AJNS_176_17
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