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Genomic inversions and GOLGA core duplicons underlie disease instability at the 15q25 locus
Human chromosome 15q25 is involved in several disease-associated structural rearrangements, including microdeletions and chromosomal markers with inverted duplications. Using comparative fluorescence in situ hybridization, strand-sequencing, single-molecule, real-time sequencing and Bionano optical...
Autores principales: | , , , , , , , , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6436712/ https://www.ncbi.nlm.nih.gov/pubmed/30917130 http://dx.doi.org/10.1371/journal.pgen.1008075 |
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author | Maggiolini, Flavia A. M. Cantsilieris, Stuart D’Addabbo, Pietro Manganelli, Michele Coe, Bradley P. Dumont, Beth L. Sanders, Ashley D. Pang, Andy Wing Chun Vollger, Mitchell R. Palumbo, Orazio Palumbo, Pietro Accadia, Maria Carella, Massimo Eichler, Evan E. Antonacci, Francesca |
author_facet | Maggiolini, Flavia A. M. Cantsilieris, Stuart D’Addabbo, Pietro Manganelli, Michele Coe, Bradley P. Dumont, Beth L. Sanders, Ashley D. Pang, Andy Wing Chun Vollger, Mitchell R. Palumbo, Orazio Palumbo, Pietro Accadia, Maria Carella, Massimo Eichler, Evan E. Antonacci, Francesca |
author_sort | Maggiolini, Flavia A. M. |
collection | PubMed |
description | Human chromosome 15q25 is involved in several disease-associated structural rearrangements, including microdeletions and chromosomal markers with inverted duplications. Using comparative fluorescence in situ hybridization, strand-sequencing, single-molecule, real-time sequencing and Bionano optical mapping analyses, we investigated the organization of the 15q25 region in human and nonhuman primates. We found that two independent inversions occurred in this region after the fission event that gave rise to phylogenetic chromosomes XIV and XV in humans and great apes. One of these inversions is still polymorphic in the human population today and may confer differential susceptibility to 15q25 microdeletions and inverted duplications. The inversion breakpoints map within segmental duplications containing core duplicons of the GOLGA gene family and correspond to the site of an ancestral centromere, which became inactivated about 25 million years ago. The inactivation of this centromere likely released segmental duplications from recombination repression typical of centromeric regions. We hypothesize that this increased the frequency of ectopic recombination creating a hotspot of hominid inversions where dispersed GOLGA core elements now predispose this region to recurrent genomic rearrangements associated with disease. |
format | Online Article Text |
id | pubmed-6436712 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2019 |
publisher | Public Library of Science |
record_format | MEDLINE/PubMed |
spelling | pubmed-64367122019-04-12 Genomic inversions and GOLGA core duplicons underlie disease instability at the 15q25 locus Maggiolini, Flavia A. M. Cantsilieris, Stuart D’Addabbo, Pietro Manganelli, Michele Coe, Bradley P. Dumont, Beth L. Sanders, Ashley D. Pang, Andy Wing Chun Vollger, Mitchell R. Palumbo, Orazio Palumbo, Pietro Accadia, Maria Carella, Massimo Eichler, Evan E. Antonacci, Francesca PLoS Genet Research Article Human chromosome 15q25 is involved in several disease-associated structural rearrangements, including microdeletions and chromosomal markers with inverted duplications. Using comparative fluorescence in situ hybridization, strand-sequencing, single-molecule, real-time sequencing and Bionano optical mapping analyses, we investigated the organization of the 15q25 region in human and nonhuman primates. We found that two independent inversions occurred in this region after the fission event that gave rise to phylogenetic chromosomes XIV and XV in humans and great apes. One of these inversions is still polymorphic in the human population today and may confer differential susceptibility to 15q25 microdeletions and inverted duplications. The inversion breakpoints map within segmental duplications containing core duplicons of the GOLGA gene family and correspond to the site of an ancestral centromere, which became inactivated about 25 million years ago. The inactivation of this centromere likely released segmental duplications from recombination repression typical of centromeric regions. We hypothesize that this increased the frequency of ectopic recombination creating a hotspot of hominid inversions where dispersed GOLGA core elements now predispose this region to recurrent genomic rearrangements associated with disease. Public Library of Science 2019-03-27 /pmc/articles/PMC6436712/ /pubmed/30917130 http://dx.doi.org/10.1371/journal.pgen.1008075 Text en © 2019 Maggiolini et al http://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/) , which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. |
spellingShingle | Research Article Maggiolini, Flavia A. M. Cantsilieris, Stuart D’Addabbo, Pietro Manganelli, Michele Coe, Bradley P. Dumont, Beth L. Sanders, Ashley D. Pang, Andy Wing Chun Vollger, Mitchell R. Palumbo, Orazio Palumbo, Pietro Accadia, Maria Carella, Massimo Eichler, Evan E. Antonacci, Francesca Genomic inversions and GOLGA core duplicons underlie disease instability at the 15q25 locus |
title | Genomic inversions and GOLGA core duplicons underlie disease instability at the 15q25 locus |
title_full | Genomic inversions and GOLGA core duplicons underlie disease instability at the 15q25 locus |
title_fullStr | Genomic inversions and GOLGA core duplicons underlie disease instability at the 15q25 locus |
title_full_unstemmed | Genomic inversions and GOLGA core duplicons underlie disease instability at the 15q25 locus |
title_short | Genomic inversions and GOLGA core duplicons underlie disease instability at the 15q25 locus |
title_sort | genomic inversions and golga core duplicons underlie disease instability at the 15q25 locus |
topic | Research Article |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6436712/ https://www.ncbi.nlm.nih.gov/pubmed/30917130 http://dx.doi.org/10.1371/journal.pgen.1008075 |
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