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Phospholamban cardiomyopathy: a Canadian perspective on a unique population

INTRODUCTION: Phospholamban cardiomyopathy is an inherited cardiomyopathy, characterised by a defect in regulation of the sarcoplasmic reticulum Ca(2+) pump, often presenting with malignant arrhythmias and progressive cardiac dysfunction occurring at a young age. METHODS: Phospholamban R14del mutati...

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Detalles Bibliográficos
Autores principales:	Cheung, C. C., Healey, J. S., Hamilton, R., Spears, D., Gollob, M. H., Mellor, G., Steinberg, C., Sanatani, S., Laksman, Z. W., Krahn, A. D.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Bohn Stafleu van Loghum 2019
Materias:	Original Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6439019/ https://www.ncbi.nlm.nih.gov/pubmed/30806910 http://dx.doi.org/10.1007/s12471-019-1247-0

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