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Delayed appearance of mature ganglia in an infant with an atypical presentation of total colonic and small bowel aganglionosis: a case report

BACKGROUND: Total colonic and small bowel aganglionosis (TCSA) occurs in less than 1% of all Hirschsprung’s disease patients. Currently, the mainstay of treatment is surgery. However, in patients with TCSA, functional outcomes are often poor. A characteristic transition zone in TCSA can be difficult...

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Detalles Bibliográficos
Autores principales:	Salimi Jazi, Fereshteh, Chandler, Julia M., Thorson, Chad M., Sinclair, Tiffany J., Hazard, Florette K., Kerner, John A., Dutta, Sanjeev, Dunn, James C.Y., Chao, Stephanie D.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2019
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6449943/ https://www.ncbi.nlm.nih.gov/pubmed/30953480 http://dx.doi.org/10.1186/s12887-019-1456-0

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