Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival

Malignant granular cell tumor (MGCT) is a rare high-grade mesenchymal tumor of Schwann cell origin. MGCTs commonly affect thigh, extremity, and trunk; however, involvement of the abdominal wall is quite rare. It has poor prognosis with 39% mortality rate in 3-year interval. We report a 50-year-old f...

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Autores principales: Alnashwan, Yara A., Ali, Khaled A. H., Amr, Samir S.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2019
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6475540/
https://www.ncbi.nlm.nih.gov/pubmed/31080684
http://dx.doi.org/10.1155/2019/9576487
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author Alnashwan, Yara A.
Ali, Khaled A. H.
Amr, Samir S.
author_facet Alnashwan, Yara A.
Ali, Khaled A. H.
Amr, Samir S.
author_sort Alnashwan, Yara A.
collection PubMed
description Malignant granular cell tumor (MGCT) is a rare high-grade mesenchymal tumor of Schwann cell origin. MGCTs commonly affect thigh, extremity, and trunk; however, involvement of the abdominal wall is quite rare. It has poor prognosis with 39% mortality rate in 3-year interval. We report a 50-year-old female who had MGCT arising in the anterior abdominal wall and developed massive metastatic deposits in both lungs and in the right inguinal lymph nodes, with prolonged survival for 11 years. A brief review of the literature is presented.
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spelling pubmed-64755402019-05-12 Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival Alnashwan, Yara A. Ali, Khaled A. H. Amr, Samir S. Case Rep Pathol Case Report Malignant granular cell tumor (MGCT) is a rare high-grade mesenchymal tumor of Schwann cell origin. MGCTs commonly affect thigh, extremity, and trunk; however, involvement of the abdominal wall is quite rare. It has poor prognosis with 39% mortality rate in 3-year interval. We report a 50-year-old female who had MGCT arising in the anterior abdominal wall and developed massive metastatic deposits in both lungs and in the right inguinal lymph nodes, with prolonged survival for 11 years. A brief review of the literature is presented. Hindawi 2019-04-07 /pmc/articles/PMC6475540/ /pubmed/31080684 http://dx.doi.org/10.1155/2019/9576487 Text en Copyright © 2019 Yara A. Alnashwan et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Alnashwan, Yara A.
Ali, Khaled A. H.
Amr, Samir S.
Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival
title Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival
title_full Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival
title_fullStr Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival
title_full_unstemmed Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival
title_short Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival
title_sort metastasizing malignant granular cell tumor (abrikossoff tumor) of the anterior abdominal wall, with prolonged survival
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6475540/
https://www.ncbi.nlm.nih.gov/pubmed/31080684
http://dx.doi.org/10.1155/2019/9576487
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