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Macrodystrophia Lipomatosa of the Finger: A Case Report

INTRODUCTION: Macrodystrophia lipomatosa is a rare benign condition characterized by a progressive persistent proliferation of the mesenchymal components and elements, with a disproportionate increase in fibro-adipose tissue. It causes a debilitating functional and psychological effect on the patien...

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Autores principales: AlArifi, Mishal, Al Essa, Ahmad, Mashour, Miral, Mohamed Aly, Ahmed, Tayara, Bader, Al Absi, Emad
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6477462/
https://www.ncbi.nlm.nih.gov/pubmed/31043943
http://dx.doi.org/10.1159/000496685
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author AlArifi, Mishal
Al Essa, Ahmad
Mashour, Miral
Mohamed Aly, Ahmed
Tayara, Bader
Al Absi, Emad
author_facet AlArifi, Mishal
Al Essa, Ahmad
Mashour, Miral
Mohamed Aly, Ahmed
Tayara, Bader
Al Absi, Emad
author_sort AlArifi, Mishal
collection PubMed
description INTRODUCTION: Macrodystrophia lipomatosa is a rare benign condition characterized by a progressive persistent proliferation of the mesenchymal components and elements, with a disproportionate increase in fibro-adipose tissue. It causes a debilitating functional and psychological effect on the patient and his family. CASE PRESENTATION: A 25-years-old male patient presented complaining of left middle finger swelling which was painless and progressive in size with no restriction of range of motion. Plain X-ray films of the left hand showed a heterogeneous lobulated soft tissue mass on the volar aspect of the middle finger which was confirmed by MRI scan. Surgery was performed by doing a left middle finger soft tissue excision and diagnosis of Macrodystrophia lipomatosa was confirmed by the histopathology report. Patient was on regular follow up in the clinic with no tumour recurrence and an excellent cosmetic as well as functional result with full finger joints range of motion. CONCLUSION: Macrodystrophia lipomatosa should be suspected with this kind of presentations. Combination of the clinical history and examination with the aid of radiological assays aided in the diagnosis of this extremely rare case and led to the appropriate management by excising this mass and restoring the normal function of the patient's hand.
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spelling pubmed-64774622019-05-01 Macrodystrophia Lipomatosa of the Finger: A Case Report AlArifi, Mishal Al Essa, Ahmad Mashour, Miral Mohamed Aly, Ahmed Tayara, Bader Al Absi, Emad Case Rep Oncol Case Report INTRODUCTION: Macrodystrophia lipomatosa is a rare benign condition characterized by a progressive persistent proliferation of the mesenchymal components and elements, with a disproportionate increase in fibro-adipose tissue. It causes a debilitating functional and psychological effect on the patient and his family. CASE PRESENTATION: A 25-years-old male patient presented complaining of left middle finger swelling which was painless and progressive in size with no restriction of range of motion. Plain X-ray films of the left hand showed a heterogeneous lobulated soft tissue mass on the volar aspect of the middle finger which was confirmed by MRI scan. Surgery was performed by doing a left middle finger soft tissue excision and diagnosis of Macrodystrophia lipomatosa was confirmed by the histopathology report. Patient was on regular follow up in the clinic with no tumour recurrence and an excellent cosmetic as well as functional result with full finger joints range of motion. CONCLUSION: Macrodystrophia lipomatosa should be suspected with this kind of presentations. Combination of the clinical history and examination with the aid of radiological assays aided in the diagnosis of this extremely rare case and led to the appropriate management by excising this mass and restoring the normal function of the patient's hand. S. Karger AG 2019-01-21 /pmc/articles/PMC6477462/ /pubmed/31043943 http://dx.doi.org/10.1159/000496685 Text en Copyright © 2019 by S. Karger AG, Basel http://creativecommons.org/licenses/by-nc/4.0/ This article is licensed under the Creative Commons Attribution-NonCommercial-4.0 International License (CC BY-NC) (http://www.karger.com/Services/OpenAccessLicense). Usage and distribution for commercial purposes requires written permission.
spellingShingle Case Report
AlArifi, Mishal
Al Essa, Ahmad
Mashour, Miral
Mohamed Aly, Ahmed
Tayara, Bader
Al Absi, Emad
Macrodystrophia Lipomatosa of the Finger: A Case Report
title Macrodystrophia Lipomatosa of the Finger: A Case Report
title_full Macrodystrophia Lipomatosa of the Finger: A Case Report
title_fullStr Macrodystrophia Lipomatosa of the Finger: A Case Report
title_full_unstemmed Macrodystrophia Lipomatosa of the Finger: A Case Report
title_short Macrodystrophia Lipomatosa of the Finger: A Case Report
title_sort macrodystrophia lipomatosa of the finger: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6477462/
https://www.ncbi.nlm.nih.gov/pubmed/31043943
http://dx.doi.org/10.1159/000496685
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