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Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient

Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely reporte...

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Autores principales: Shih, Beatrice Chia-Hui, Lim, Jae Hong, Min, Jooncheol, Kim, Eung Re, Kwak, Jae Gun, Kim, Woong-Han
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Society for Thoracic and Cardiovascular Surgery 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6493263/
https://www.ncbi.nlm.nih.gov/pubmed/31089447
http://dx.doi.org/10.5090/kjtcs.2019.52.2.100
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author Shih, Beatrice Chia-Hui
Lim, Jae Hong
Min, Jooncheol
Kim, Eung Re
Kwak, Jae Gun
Kim, Woong-Han
author_facet Shih, Beatrice Chia-Hui
Lim, Jae Hong
Min, Jooncheol
Kim, Eung Re
Kwak, Jae Gun
Kim, Woong-Han
author_sort Shih, Beatrice Chia-Hui
collection PubMed
description Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely reported in the literature, meaning that insufficient general data exist concerning the surgical strategy and clinical follow-up. Herein, we report the case of a 31-year-old woman with a diagnosis of incomplete form of Shone complex with parachute mitral valve and coarctation of the aorta who underwent successful single-stage surgical repair.
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spelling pubmed-64932632019-05-14 Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient Shih, Beatrice Chia-Hui Lim, Jae Hong Min, Jooncheol Kim, Eung Re Kwak, Jae Gun Kim, Woong-Han Korean J Thorac Cardiovasc Surg Case Report Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely reported in the literature, meaning that insufficient general data exist concerning the surgical strategy and clinical follow-up. Herein, we report the case of a 31-year-old woman with a diagnosis of incomplete form of Shone complex with parachute mitral valve and coarctation of the aorta who underwent successful single-stage surgical repair. The Korean Society for Thoracic and Cardiovascular Surgery 2019-04 2019-04-05 /pmc/articles/PMC6493263/ /pubmed/31089447 http://dx.doi.org/10.5090/kjtcs.2019.52.2.100 Text en Copyright © 2019 by The Korean Society for Thoracic and Cardiovascular Surgery. All rights Reserved. This is an open access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Shih, Beatrice Chia-Hui
Lim, Jae Hong
Min, Jooncheol
Kim, Eung Re
Kwak, Jae Gun
Kim, Woong-Han
Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient
title Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient
title_full Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient
title_fullStr Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient
title_full_unstemmed Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient
title_short Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient
title_sort incomplete form of shone complex in an adult congenital heart disease patient
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6493263/
https://www.ncbi.nlm.nih.gov/pubmed/31089447
http://dx.doi.org/10.5090/kjtcs.2019.52.2.100
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