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Impaired fat oxidation during exercise in multiple acyl‐CoA dehydrogenase deficiency

We investigated the in vivo skeletal muscle metabolism in patients with multiple acyl‐CoA dehydrogenase deficiency (MADD) during exercise, and the effect of a glucose infusion. Two adults with MADD on riboflavin and l‐carnitine treatment and 10 healthy controls performed an incremental exercise test...

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Detalles Bibliográficos
Autores principales:	Madsen, Karen L., Preisler, Nicolai, Buch, Astrid E., Stemmerik, Mads G., Laforêt, Pascal, Vissing, John
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley & Sons, Inc. 2019
Materias:	Research Reports
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6498824/ https://www.ncbi.nlm.nih.gov/pubmed/31240159 http://dx.doi.org/10.1002/jmd2.12024

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