Relapsed papillary urothelial neoplasm of low malignant potential (PUNLMP) of the young age: a case report and a review of the literature

BACKGROUND: Papillary Urothelial Neoplasm of Low Malignant Potential (PUNLMP) are exceptionally rare in the first decade of life (mostly if multifocal) and there is a lack of standardized recommendations for the pediatric age. CASE PRESENTATION: We describe the case of a 9-year-old boy with a diagno...

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Autores principales: Maurizi, Palma, Capozza, Michele Antonio, Triarico, Silvia, Perrotta, Maria Luisa, Briganti, Vito, Ruggiero, Antonio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2019
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6509853/
https://www.ncbi.nlm.nih.gov/pubmed/31072376
http://dx.doi.org/10.1186/s12894-019-0469-1
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author Maurizi, Palma
Capozza, Michele Antonio
Triarico, Silvia
Perrotta, Maria Luisa
Briganti, Vito
Ruggiero, Antonio
author_facet Maurizi, Palma
Capozza, Michele Antonio
Triarico, Silvia
Perrotta, Maria Luisa
Briganti, Vito
Ruggiero, Antonio
author_sort Maurizi, Palma
collection PubMed
description BACKGROUND: Papillary Urothelial Neoplasm of Low Malignant Potential (PUNLMP) are exceptionally rare in the first decade of life (mostly if multifocal) and there is a lack of standardized recommendations for the pediatric age. CASE PRESENTATION: We describe the case of a 9-year-old boy with a diagnosis of PUNLMP, who underwent to cystoscopic lesion removal and later to endoscopic lesion removal and intra-bladder Mitomycin-c (MMC) instillations for relapsed disease. Follow-up investigations at five years showed disease negativity. CONCLUSIONS: Intra-bladder MMC instillation may allow obtaining the complete remission with bladder-sparing for paediatric patients with a high-risk relapsed PUNLMP.
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spelling pubmed-65098532019-06-05 Relapsed papillary urothelial neoplasm of low malignant potential (PUNLMP) of the young age: a case report and a review of the literature Maurizi, Palma Capozza, Michele Antonio Triarico, Silvia Perrotta, Maria Luisa Briganti, Vito Ruggiero, Antonio BMC Urol Case Report BACKGROUND: Papillary Urothelial Neoplasm of Low Malignant Potential (PUNLMP) are exceptionally rare in the first decade of life (mostly if multifocal) and there is a lack of standardized recommendations for the pediatric age. CASE PRESENTATION: We describe the case of a 9-year-old boy with a diagnosis of PUNLMP, who underwent to cystoscopic lesion removal and later to endoscopic lesion removal and intra-bladder Mitomycin-c (MMC) instillations for relapsed disease. Follow-up investigations at five years showed disease negativity. CONCLUSIONS: Intra-bladder MMC instillation may allow obtaining the complete remission with bladder-sparing for paediatric patients with a high-risk relapsed PUNLMP. BioMed Central 2019-05-09 /pmc/articles/PMC6509853/ /pubmed/31072376 http://dx.doi.org/10.1186/s12894-019-0469-1 Text en © The Author(s). 2019 Open Access This article is distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.
spellingShingle Case Report
Maurizi, Palma
Capozza, Michele Antonio
Triarico, Silvia
Perrotta, Maria Luisa
Briganti, Vito
Ruggiero, Antonio
Relapsed papillary urothelial neoplasm of low malignant potential (PUNLMP) of the young age: a case report and a review of the literature
title Relapsed papillary urothelial neoplasm of low malignant potential (PUNLMP) of the young age: a case report and a review of the literature
title_full Relapsed papillary urothelial neoplasm of low malignant potential (PUNLMP) of the young age: a case report and a review of the literature
title_fullStr Relapsed papillary urothelial neoplasm of low malignant potential (PUNLMP) of the young age: a case report and a review of the literature
title_full_unstemmed Relapsed papillary urothelial neoplasm of low malignant potential (PUNLMP) of the young age: a case report and a review of the literature
title_short Relapsed papillary urothelial neoplasm of low malignant potential (PUNLMP) of the young age: a case report and a review of the literature
title_sort relapsed papillary urothelial neoplasm of low malignant potential (punlmp) of the young age: a case report and a review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6509853/
https://www.ncbi.nlm.nih.gov/pubmed/31072376
http://dx.doi.org/10.1186/s12894-019-0469-1
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