Cargando…

Unraveling the CFTR Function–Phenotype Connection for Precision Treatment in Cystic Fibrosis

Detalles Bibliográficos
Autores principales:	Zemanick, Edith T., Polineni, Deepika
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	American Thoracic Society 2019
Materias:	Editorials
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6515879/ https://www.ncbi.nlm.nih.gov/pubmed/30939246 http://dx.doi.org/10.1164/rccm.201903-0696ED

Ejemplares similares

Evidence for Early Cystic Fibrosis Transmembrane Conductance Regulator Modulator Treatment for Children with Cystic Fibrosis Keeps Growing
por: Hoppe, Jordana E., et al.
Publicado: (2022)

CFTR Modulators: Shedding Light on Precision Medicine for Cystic Fibrosis
por: Lopes-Pacheco, Miquéias
Publicado: (2016)

Precision Medicine Based on CFTR Genotype for People with Cystic Fibrosis
por: Haq, Iram, et al.
Publicado: (2022)

Urinary Exosomes of Patients with Cystic Fibrosis Unravel CFTR-Related Renal Disease
por: Gauthier, Sebastien, et al.
Publicado: (2020)

Cystic Fibrosis and Cancer: Unraveling the Complex Role of CFTR Gene in Cancer Susceptibility
por: Parisi, Giuseppe Fabio, et al.
Publicado: (2023)

Fungal Infection and Inflammation in Cystic Fibrosis
por: Poore, T. Spencer, et al.
Publicado: (2021)

CFTR Modulators: The Changing Face of Cystic Fibrosis in the Era of Precision Medicine
por: Lopes-Pacheco, Miquéias
Publicado: (2020)

CFTR Modulators to the Rescue of Individuals with Cystic Fibrosis and Advanced Lung Disease
por: Myerburg, Mike, et al.
Publicado: (2021)

Infection, Allergy, and Inflammation: The Role of Aspergillus fumigatus in Cystic Fibrosis
por: Poore, T. Spencer, et al.
Publicado: (2023)

Aztreonam Lysine Inhalation Solution in Cystic Fibrosis
por: Elson, Elizabeth Claire, et al.
Publicado: (2019)

Progress in precision medicine in cystic fibrosis: a focus on CFTR modulator therapy
por: Tewkesbury, Daniel H., et al.
Publicado: (2021)

Airway microbial diversity is decreased in young children with cystic fibrosis compared to healthy controls but improved with CFTR modulation
por: Hahn, Andrea, et al.
Publicado: (2020)

Targeted therapies to improve CFTR function in cystic fibrosis
por: Brodlie, Malcolm, et al.
Publicado: (2015)

Cystic Fibrosis, CFTR, and Colorectal Cancer
por: Scott, Patricia, et al.
Publicado: (2020)

How Should the Effects of CFTR Modulator Therapy on Cystic Fibrosis Lung Disease Be Monitored?
por: Ben-Meir, Elad, et al.
Publicado: (2022)

The P2X7 Receptor in Cystic Fibrosis Monocytes: Linking CFTR Deficiency to Inflammation
por: Cantin, André M.
Publicado: (2022)

Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutation
por: Stefano, Daniela De, et al.
Publicado: (2014)

The importance of CFTR expression for neutrophil function in patients with Cystic Fibrosis
por: Jundi, B, et al.
Publicado: (2015)

Triplet CFTR modulators: future prospects for treatment of cystic fibrosis
por: Chaudary, Nauman
Publicado: (2018)

CFTR and Ca(2+) Signaling in Cystic Fibrosis
por: Antigny, Fabrice, et al.
Publicado: (2011)

Strategies to circumvent the CFTR defect in cystic fibrosis
por: Becq, Frédéric, et al.
Publicado: (2013)

Not All Is CFTR – Neutrophils and Cholesterol in Cystic Fibrosis
por: Castellani, Stefano, et al.
Publicado: (2017)

Cystic Fibrosis and Oxidative Stress: The Role of CFTR
por: Moliteo, Evelina, et al.
Publicado: (2022)

CFTR modulators: transformative therapies for cystic fibrosis
por: Dwight, Mary, et al.
Publicado: (2021)

Unravelling the Regions of Mutant F508del-CFTR More Susceptible to the Action of Four Cystic Fibrosis Correctors
por: Amico, Giulia, et al.
Publicado: (2019)

'CFTR-opathies': disease phenotypes associated with cystic fibrosis transmembrane regulator gene mutations
por: Noone, Peadar G, et al.
Publicado: (2001)

Validation of nasospheroids to assay CFTR functionality and modulator responses in cystic fibrosis
por: Calucho, Maite, et al.
Publicado: (2021)

Cystic fibrosis transmembrane conductance regulator (CFTR) modulators have differential effects on cystic fibrosis macrophage function
por: Zhang, Shuzhong, et al.
Publicado: (2018)

Long-term effectiveness of dual CFTR modulator treatment of cystic fibrosis
por: Muilwijk, Danya, et al.
Publicado: (2022)

Inflammation and CFTR: might neutrophils be the key in cystic fibrosis?
por: Witko-Sarsat, V, et al.
Publicado: (1999)

Fixing cystic fibrosis by correcting CFTR domain assembly
por: Okiyoneda, Tsukasa, et al.
Publicado: (2012)

Lived experiences of individuals with cystic fibrosis on CFTR-modulators
por: Page, Annelise, et al.
Publicado: (2022)

The Effect of CFTR Modulators on Airway Infection in Cystic Fibrosis
por: Harvey, Caitlyn, et al.
Publicado: (2022)

Nutritional impact of CFTR modulators in children with cystic fibrosis
por: Gaschignard, Margaux, et al.
Publicado: (2023)

Cross‐talk between CFTR and sphingolipids in cystic fibrosis
por: Dobi, Dorina, et al.
Publicado: (2023)

Bicarbonate and functional CFTR channel are required for proper mucin secretion and link cystic fibrosis with its mucus phenotype
por: Gustafsson, Jenny K., et al.
Publicado: (2012)

Ivacaftor modifies cystic fibrosis neutrophil phenotype in subjects with R117H residual function CFTR mutations
por: Hardisty, Gareth R., et al.
Publicado: (2021)

Change in circulating proteins during treatment of pulmonary exacerbation in patients with cystic fibrosis
por: Wagner, Brandie D., et al.
Publicado: (2021)

The Need for Precision Therapies as Determined by Genetic Signature for Cystic Fibrosis
por: Zahir, Farah R.
Publicado: (2021)

Phenotyping ciliary dynamics and coordination in response to CFTR-modulators in Cystic Fibrosis respiratory epithelial cells
por: Chioccioli, M., et al.
Publicado: (2019)

Cannot write session to /tmp/vufind_sessions/sess_bm7uo6t5kqr01b3hug91lsg4l6