Fibrosarcoma of the ethmoid sinus: A rare entity

INTRODUCTION: Ethmoidal fibrosarcoma is an extremely rare tumor which represent less than one percent of all malignancies in this anatomical area, the case of a 13-year-old is reported here. PRESENTATION OF CASE: A 13-year-old boy, his medical history was marked exclusively before presented to our hospital by an exophthalmia. Rhinoscopic examination showed well-defined pink mass at the level of ethmoid. Computed tomography was performed to showed local and regional extension. Treatment was an endoscopic excision of the tumor using a navigation system. The final diagnosis was made on pathologic examination. Radiotherapy was recommended by multidisciplinary staff but the patient refused. DISCUSSION: These tumors occur in extremities most frequently and Ethmoidal localization is extremely rare and have no specifics symptoms, so the rhinoscopic examination is necessary for any chronic nasal symptom. Its treatment is not codified because of its rarity and its prognosis is unknown. CONCLUSION: It’s important knowledge about this pathology because of its rarity and its therapeutic and prognostic difficulties.