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Persistent pruritus as a rare and potentially serious manifestation of liver involvement in autosomal dominant polycystic kidney disease

Polycystic liver disease (PCLD) is the most frequent extrarenal manifestation of autosomal dominant polycystic kidney disease (ADPKD), usually asymptomatic. We present a patient with ADPKD who developed cholestatic pruritus due to bile duct compression of multiple liver cysts. Because of severity of...

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Detalles Bibliográficos
Autores principales:	García-Prieto, Ana, Torres, Esther, Hernández, Andrés, Barbieri, Diego, Vega, Almudena
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Oxford University Press 2018
Materias:	Genetic Kidney Disease
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6543959/ https://www.ncbi.nlm.nih.gov/pubmed/31198538 http://dx.doi.org/10.1093/ckj/sfy057

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