Efficacy of pentosan polysulfate in in vitro models of lysosomal storage disorders: Fabry and Gaucher Disease

Gaucher and Fabry diseases are the most prevalent sphingolipidoses. Chronic inflammation is activated in those disorders, which could play a role in pathogenesis. Significant degrees of amelioration occur in patients upon introduction of specific therapies; however, restoration to complete health st...

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Detalles Bibliográficos
Autores principales: Crivaro, Andrea N., Mucci, Juan M., Bondar, Constanza M., Ormazabal, Maximiliano E., Ceci, Romina, Simonaro, Calogera, Rozenfeld, Paula A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2019
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6544267/
https://www.ncbi.nlm.nih.gov/pubmed/31150494
http://dx.doi.org/10.1371/journal.pone.0217780

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6544267/
https://www.ncbi.nlm.nih.gov/pubmed/31150494
http://dx.doi.org/10.1371/journal.pone.0217780

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