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Hearing Dysfunction in a Large Family Affected by Dominant Optic Atrophy (OPA8-Related DOA): A Human Model of Hidden Auditory Neuropathy

Hidden auditory neuropathy is characterized by reduced performances in challenging auditory tasks with the preservation of hearing thresholds, resulting from diffuse loss of cochlear inner hair cell (IHC) synapses following primary degeneration of unmyelinated terminals of auditory fibers. We report...

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Detalles Bibliográficos
Autores principales:	Santarelli, Rosamaria, La Morgia, Chiara, Valentino, Maria Lucia, Barboni, Piero, Monteleone, Anna, Scimemi, Pietro, Carelli, Valerio
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2019
Materias:	Neuroscience
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6546873/ https://www.ncbi.nlm.nih.gov/pubmed/31191217 http://dx.doi.org/10.3389/fnins.2019.00501

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