Cargando…

Bilateral pheochromocytoma after kidney transplantation in neurofibromatosis type 1

We present the case of a 25-year-old male with a history of neurofibromatosis type 1 and bilateral pheochromocytoma 4 years after kidney transplantation that was successfully treated with simultaneous bilateral posterior retroperitoneoscopic adrenalectomy. LEARNING POINTS: Hypertensive patients with...

Descripción completa

Detalles Bibliográficos
Autores principales: de Miguel, Valeria, Paissan, Andrea, García Marchiñena, Patricio, Jurado, Alberto, Isola, Mariana, Alfie, José, Fainstein-Day, Patricia
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Bioscientifica Ltd 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6548217/
https://www.ncbi.nlm.nih.gov/pubmed/31125973
http://dx.doi.org/10.1530/EDM-18-0162
_version_ 1783423821516111872
author de Miguel, Valeria
Paissan, Andrea
García Marchiñena, Patricio
Jurado, Alberto
Isola, Mariana
Alfie, José
Fainstein-Day, Patricia
author_facet de Miguel, Valeria
Paissan, Andrea
García Marchiñena, Patricio
Jurado, Alberto
Isola, Mariana
Alfie, José
Fainstein-Day, Patricia
author_sort de Miguel, Valeria
collection PubMed
description We present the case of a 25-year-old male with a history of neurofibromatosis type 1 and bilateral pheochromocytoma 4 years after kidney transplantation that was successfully treated with simultaneous bilateral posterior retroperitoneoscopic adrenalectomy. LEARNING POINTS: Hypertensive patients with NF1 should always be screened for pheochromocytoma. Pheochromocytoma is rarely associated with transplantation, but it must be ruled out in patients with genetic susceptibility. Posterior retroperitoneoscopic adrenalectomy (PRA) allows more direct access to the adrenal glands, especially in patients with previous abdominal surgeries.
format Online
Article
Text
id pubmed-6548217
institution National Center for Biotechnology Information
language English
publishDate 2019
publisher Bioscientifica Ltd
record_format MEDLINE/PubMed
spelling pubmed-65482172019-06-12 Bilateral pheochromocytoma after kidney transplantation in neurofibromatosis type 1 de Miguel, Valeria Paissan, Andrea García Marchiñena, Patricio Jurado, Alberto Isola, Mariana Alfie, José Fainstein-Day, Patricia Endocrinol Diabetes Metab Case Rep Insight into Disease Pathogenesis or Mechanism of Therapy We present the case of a 25-year-old male with a history of neurofibromatosis type 1 and bilateral pheochromocytoma 4 years after kidney transplantation that was successfully treated with simultaneous bilateral posterior retroperitoneoscopic adrenalectomy. LEARNING POINTS: Hypertensive patients with NF1 should always be screened for pheochromocytoma. Pheochromocytoma is rarely associated with transplantation, but it must be ruled out in patients with genetic susceptibility. Posterior retroperitoneoscopic adrenalectomy (PRA) allows more direct access to the adrenal glands, especially in patients with previous abdominal surgeries. Bioscientifica Ltd 2019-05-23 /pmc/articles/PMC6548217/ /pubmed/31125973 http://dx.doi.org/10.1530/EDM-18-0162 Text en © 2019 The authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. (http://creativecommons.org/licenses/by-nc-nd/4.0/) .
spellingShingle Insight into Disease Pathogenesis or Mechanism of Therapy
de Miguel, Valeria
Paissan, Andrea
García Marchiñena, Patricio
Jurado, Alberto
Isola, Mariana
Alfie, José
Fainstein-Day, Patricia
Bilateral pheochromocytoma after kidney transplantation in neurofibromatosis type 1
title Bilateral pheochromocytoma after kidney transplantation in neurofibromatosis type 1
title_full Bilateral pheochromocytoma after kidney transplantation in neurofibromatosis type 1
title_fullStr Bilateral pheochromocytoma after kidney transplantation in neurofibromatosis type 1
title_full_unstemmed Bilateral pheochromocytoma after kidney transplantation in neurofibromatosis type 1
title_short Bilateral pheochromocytoma after kidney transplantation in neurofibromatosis type 1
title_sort bilateral pheochromocytoma after kidney transplantation in neurofibromatosis type 1
topic Insight into Disease Pathogenesis or Mechanism of Therapy
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6548217/
https://www.ncbi.nlm.nih.gov/pubmed/31125973
http://dx.doi.org/10.1530/EDM-18-0162
work_keys_str_mv AT demiguelvaleria bilateralpheochromocytomaafterkidneytransplantationinneurofibromatosistype1
AT paissanandrea bilateralpheochromocytomaafterkidneytransplantationinneurofibromatosistype1
AT garciamarchinenapatricio bilateralpheochromocytomaafterkidneytransplantationinneurofibromatosistype1
AT juradoalberto bilateralpheochromocytomaafterkidneytransplantationinneurofibromatosistype1
AT isolamariana bilateralpheochromocytomaafterkidneytransplantationinneurofibromatosistype1
AT alfiejose bilateralpheochromocytomaafterkidneytransplantationinneurofibromatosistype1
AT fainsteindaypatricia bilateralpheochromocytomaafterkidneytransplantationinneurofibromatosistype1