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Systemic Epstein–Barr Virus-Positive T/NK Lymphoproliferative Diseases With SH2D1A/XIAP Hypomorphic Gene Variants
X-linked lymphoproliferative disease (XLP) is one of the X-linked primary immunodeficiency diseases (PIDs) with defective immune response to Epstein–Barr virus (EBV) infection. Chronic active EBV infection (CAEBV) and EBV-hemophagocytic lymphohistiocytosis (HLH) are recognized as systemic EBV-positi...
Autores principales: | Ishimura, Masataka, Eguchi, Katsuhide, Shiraishi, Akira, Sonoda, Motoshi, Azuma, Yoshihiro, Yamamoto, Hiroyuki, Imadome, Ken-ichi, Ohga, Shouichi |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6558365/ https://www.ncbi.nlm.nih.gov/pubmed/31231620 http://dx.doi.org/10.3389/fped.2019.00183 |
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