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Over Restriction of Dietary Protein Allowance: The Importance of Ongoing Reassessment of Natural Protein Tolerance in Phenylketonuria

Phenylalanine (Phe) tolerance is highly variable in phenylketonuria (PKU) and rarely described in patients aged ≥12 years. Patients ≥12 years of age with PKU were systematically challenged with additional natural protein (NP) if blood Phe levels remained below 480 µmol/L (i.e., upper target blood Ph...

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Detalles Bibliográficos
Autores principales:	Pinto, Alex, Ferreira Almeida, Manuela, MacDonald, Anita, Cristina Ramos, Paula, Rocha, Sara, Guimas, Arlindo, Ribeiro, Rosa, Martins, Esmeralda, Bandeira, Anabela, Jackson, Richard, van Spronsen, Francjan, Payne, Anne, César Rocha, Júlio
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2019
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6566391/ https://www.ncbi.nlm.nih.gov/pubmed/31052331 http://dx.doi.org/10.3390/nu11050995

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