Cargando…

Cyclophilin A in Arrhythmogenic Cardiomyopathy Cardiac Remodeling

Arrhythmogenic cardiomyopathy (ACM) is a genetic disorder characterized by the progressive substitution of functional myocardium with noncontractile fibro-fatty tissue contributing to ventricular arrhythmias and sudden cardiac death. Cyclophilin A (CyPA) is a ubiquitous protein involved in several p...

Descripción completa

Detalles Bibliográficos
Autores principales:	Rurali, Erica, Pilato, Chiara Assunta, Perrucci, Gianluca Lorenzo, Scopece, Alessandro, Stadiotti, Ilaria, Moschetta, Donato, Casella, Michela, Cogliati, Elisa, Sommariva, Elena, Pompilio, Giulio, Nigro, Patrizia
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2019
Materias:	Communication
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6566687/ https://www.ncbi.nlm.nih.gov/pubmed/31096574 http://dx.doi.org/10.3390/ijms20102403

Ejemplares similares

Fibrosis in Arrhythmogenic Cardiomyopathy: The Phantom Thread in the Fibro-Adipose Tissue
por: Maione, Angela Serena, et al.
Publicado: (2020)

Arrhythmogenic Cardiomyopathy: the Guilty Party in Adipogenesis
por: Stadiotti, Ilaria, et al.
Publicado: (2017)

Cell models of arrhythmogenic cardiomyopathy: advances and opportunities
por: Sommariva, Elena, et al.
Publicado: (2017)

Excess TGF-β1 Drives Cardiac Mesenchymal Stromal Cells to a Pro-Fibrotic Commitment in Arrhythmogenic Cardiomyopathy
por: Maione, Angela Serena, et al.
Publicado: (2021)

Isolation and Characterization of Cardiac Mesenchymal Stromal Cells from Endomyocardial Bioptic Samples of Arrhythmogenic Cardiomyopathy Patients
por: Pilato, Chiara Assunta, et al.
Publicado: (2018)

Calcium as a Key Player in Arrhythmogenic Cardiomyopathy: Adhesion Disorder or Intracellular Alteration?
por: Moccia, Francesco, et al.
Publicado: (2019)

Cardiac Biomarkers and Autoantibodies in Endurance Athletes: Potential Similarities with Arrhythmogenic Cardiomyopathy Pathogenic Mechanisms
por: Stadiotti, Ilaria, et al.
Publicado: (2021)

Clinical and Molecular Data Define a Diagnosis of Arrhythmogenic Cardiomyopathy in a Carrier of a Brugada-Syndrome-Associated PKP2 Mutation
por: Persampieri, Simone, et al.
Publicado: (2020)

Cyclophilin A/EMMPRIN Axis Is Involved in Pro-Fibrotic Processes Associated with Thoracic Aortic Aneurysm of Marfan Syndrome Patients
por: Perrucci, Gianluca L., et al.
Publicado: (2020)

Metabolic Signature of Arrhythmogenic Cardiomyopathy
por: Volani, Chiara, et al.
Publicado: (2021)

Oxidized LDL‐dependent pathway as new pathogenic trigger in arrhythmogenic cardiomyopathy
por: Sommariva, Elena, et al.
Publicado: (2021)

Soluble EMMPRIN levels discriminate aortic ectasia in Marfan syndrome patients
por: Rurali, Erica, et al.
Publicado: (2019)

Exploring digenic inheritance in arrhythmogenic cardiomyopathy
por: König, Eva, et al.
Publicado: (2017)

Ca(2+) dysregulation in cardiac stromal cells sustains fibro-adipose remodeling in Arrhythmogenic Cardiomyopathy and can be modulated by flecainide
por: Maione, Angela S., et al.
Publicado: (2022)

Cardiac mesenchymal stromal cells are a source of adipocytes in arrhythmogenic cardiomyopathy
por: Sommariva, E., et al.
Publicado: (2016)

Spectrum of Rare and Common Genetic Variants in Arrhythmogenic Cardiomyopathy Patients
por: Lippi, Melania, et al.
Publicado: (2022)

The arrhythmogenic cardiomyopathy-specific coding and non-coding transcriptome in human cardiac stromal cells
por: Rainer, Johannes, et al.
Publicado: (2018)

MiR-320a as a Potential Novel Circulating Biomarker of Arrhythmogenic CardioMyopathy
por: Sommariva, Elena, et al.
Publicado: (2017)

Endomyocardial Biopsy: The Forgotten Piece in the Arrhythmogenic Cardiomyopathy Puzzle
por: Casella, Michela, et al.
Publicado: (2021)

Human Cell Modeling for Cardiovascular Diseases
por: Lippi, Melania, et al.
Publicado: (2020)

Differences in Mitochondrial Membrane Potential Identify Distinct Populations of Human Cardiac Mesenchymal Progenitor Cells
por: Gambini, Elisa, et al.
Publicado: (2020)

Human Cardiac Mesenchymal Stromal Cells From Right and Left Ventricles Display Differences in Number, Function, and Transcriptomic Profile
por: Stadiotti, Ilaria, et al.
Publicado: (2020)

GCN5 contributes to intracellular lipid accumulation in human primary cardiac stromal cells from patients affected by Arrhythmogenic cardiomyopathy
por: Volani, Chiara, et al.
Publicado: (2022)

Fibro-fatty remodelling in arrhythmogenic cardiomyopathy
por: Kohela, Arwa, et al.
Publicado: (2022)

Patient-specific primary and pluripotent stem cell-derived stromal cells recapitulate key aspects of arrhythmogenic cardiomyopathy
por: Maione, Angela Serena, et al.
Publicado: (2023)

Derivation of human induced pluripotent stem cell line EURACi004-A from skin fibroblasts of a patient with Arrhythmogenic Cardiomyopathy carrying the heterozygous PKP2 mutation c.2569_3018del50
por: Ermon, Benedetta, et al.
Publicado: (2018)

Young at Heart: Pioneering Approaches to Model Nonischaemic Cardiomyopathy with Induced Pluripotent Stem Cells
por: Gowran, Aoife, et al.
Publicado: (2016)

Pressure Overload Activates DNA-Damage Response in Cardiac Stromal Cells: A Novel Mechanism Behind Heart Failure With Preserved Ejection Fraction?
por: Stadiotti, Ilaria, et al.
Publicado: (2022)

Cyclophilin A: a key player for human disease
por: Nigro, P, et al.
Publicado: (2013)

Arrhythmogenic cardiomyopathy
por: Pilichou, Kalliopi, et al.
Publicado: (2016)

Mechanotransduction and Adrenergic Stimulation in Arrhythmogenic Cardiomyopathy: An Overview of in vitro and in vivo Models
por: Beffagna, Giorgia, et al.
Publicado: (2020)

Scarring/arrhythmogenic cardiomyopathy
por: Corrado, Domenico, et al.
Publicado: (2023)

Sildenafil attenuates hypoxic pulmonary remodelling by inhibiting bone marrow progenitor cells
por: Favre, Shirley, et al.
Publicado: (2016)

Exercise-induced arrhythmogenic right ventricular cardiomyopathy: Reverse remodeling with detraining
por: Darden, Douglas, et al.
Publicado: (2022)

From bedside to the bench: patient-specific hiPSC-EC models uncover endothelial dysfunction in genetic cardiomyopathies
por: Rabino, Martina, et al.
Publicado: (2023)

Pregnancy in arrhythmogenic cardiomyopathy
por: Wichter, Thomas, et al.
Publicado: (2021)

Arrhythmic risk prediction in arrhythmogenic right ventricular cardiomyopathy: external validation of the arrhythmogenic right ventricular cardiomyopathy risk calculator( )
por: Jordà, Paloma, et al.
Publicado: (2022)

Modeling Cardiomyopathies in a Dish: State-of-the-Art and Novel Perspectives on hiPSC-Derived Cardiomyocytes Maturation
por: Lodola, Francesco, et al.
Publicado: (2021)

Evolving Diagnostic Criteria for Arrhythmogenic Cardiomyopathy
por: Corrado, Domenico, et al.
Publicado: (2021)

Arrhythmogenic Cardiomyopathy—Current Treatment and Future Options
por: Migliore, Federico, et al.
Publicado: (2021)

Cannot write session to /tmp/vufind_sessions/sess_aha2n0idv2f5i8hoo5v151ohb5