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Severe pulmonary disease in an adult primary ciliary dyskinesia population in Brazil

Primary Ciliary Dyskinesia (PCD) is underdiagnosed in Brazil. We enrolled patients from an adult service of Bronchiectasis over a two-year period in a cross-sectional study. The inclusion criteria were laterality disorders (LD), cough with recurrent infections and the exclusion of other causes of br...

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Detalles Bibliográficos
Autores principales:	Olm, Mary Anne Kowal, Marson, Fernando Augusto Lima, Athanazio, Rodrigo Abensur, Nakagawa, Naomi Kondo, Macchione, Mariangela, Loges, Niki Tomas, Omran, Heymut, Rached, Samia Zahi, Bertuzzo, Carmen Sílvia, Stelmach, Rafael, Saldiva, Paulo Hilário Nascimento, Ribeiro, José Dirceu, Jones, Marcus Herbert, Mauad, Thais
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Nature Publishing Group UK 2019
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6582273/ https://www.ncbi.nlm.nih.gov/pubmed/31213628 http://dx.doi.org/10.1038/s41598-019-45017-1

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