Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up

Infantile fibrosarcoma (IFS) is a malignant tumor, commonly presenting in long bones and seldom encountered after 2 years of age. It is extremely rare in the faciomaxillary region. The condition is often mistaken for teratomas, and histopathology/immunohistochemistry is confirmatory. Treatment invol...

Descripción completa

Detalles Bibliográficos
Autores principales: Jayakumar, Naveenkumar, Rathnaprabhu, Veerabahu, Ramesh, Singaravelu
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2019
Materias:
Case Report - Tumor
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6585220/
https://www.ncbi.nlm.nih.gov/pubmed/31293956
http://dx.doi.org/10.4103/ams.ams_281_18
_version_ 1783428663970103296
author Jayakumar, Naveenkumar
Rathnaprabhu, Veerabahu
Ramesh, Singaravelu
author_facet Jayakumar, Naveenkumar
Rathnaprabhu, Veerabahu
Ramesh, Singaravelu
author_sort Jayakumar, Naveenkumar
collection PubMed
description Infantile fibrosarcoma (IFS) is a malignant tumor, commonly presenting in long bones and seldom encountered after 2 years of age. It is extremely rare in the faciomaxillary region. The condition is often mistaken for teratomas, and histopathology/immunohistochemistry is confirmatory. Treatment involves surgical resection as primary modality. Prognosis is much better compared to the adult variant with even scope for spontaneous regression following “conservative” resection. We present a case of IFS of the nasomaxillary complex in a 3-month-old female child. We managed our case with surgical resection, and the patient has remained disease free for over 2 years.
format Online
Article
Text
id pubmed-6585220
institution National Center for Biotechnology Information
language English
publishDate 2019
publisher Wolters Kluwer - Medknow
record_format MEDLINE/PubMed
spelling pubmed-65852202019-07-10 Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up Jayakumar, Naveenkumar Rathnaprabhu, Veerabahu Ramesh, Singaravelu Ann Maxillofac Surg Case Report - Tumor Infantile fibrosarcoma (IFS) is a malignant tumor, commonly presenting in long bones and seldom encountered after 2 years of age. It is extremely rare in the faciomaxillary region. The condition is often mistaken for teratomas, and histopathology/immunohistochemistry is confirmatory. Treatment involves surgical resection as primary modality. Prognosis is much better compared to the adult variant with even scope for spontaneous regression following “conservative” resection. We present a case of IFS of the nasomaxillary complex in a 3-month-old female child. We managed our case with surgical resection, and the patient has remained disease free for over 2 years. Wolters Kluwer - Medknow 2019 /pmc/articles/PMC6585220/ /pubmed/31293956 http://dx.doi.org/10.4103/ams.ams_281_18 Text en Copyright: © 2019 Annals of Maxillofacial Surgery http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report - Tumor
Jayakumar, Naveenkumar
Rathnaprabhu, Veerabahu
Ramesh, Singaravelu
Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up
title Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up
title_full Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up
title_fullStr Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up
title_full_unstemmed Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up
title_short Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up
title_sort preliminary report of a true nasomaxillary infantile fibrosarcoma: single-modality management and 2-year follow-up
topic Case Report - Tumor
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6585220/
https://www.ncbi.nlm.nih.gov/pubmed/31293956
http://dx.doi.org/10.4103/ams.ams_281_18
work_keys_str_mv AT jayakumarnaveenkumar preliminaryreportofatruenasomaxillaryinfantilefibrosarcomasinglemodalitymanagementand2yearfollowup
AT rathnaprabhuveerabahu preliminaryreportofatruenasomaxillaryinfantilefibrosarcomasinglemodalitymanagementand2yearfollowup
AT rameshsingaravelu preliminaryreportofatruenasomaxillaryinfantilefibrosarcomasinglemodalitymanagementand2yearfollowup

Ejemplares similares