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Development of a Desmocollin-3 Active Mouse Model Recapitulating Human Atypical Pemphigus
Pemphigus vulgaris (PV) is a life-threatening mucocutaneous autoimmune blistering disease. It is often associated with autoantibodies to the desmosomal adhesion proteins Desmoglein 3 (DSG3) and Desmoglein 1 (DSG1). Recently, auto-antigens, such as desmocollins and others have been described in PV an...
Autores principales: | Lotti, Roberta, Atene, Claudio Giacinto, Marconi, Alessandra, Di Rocco, Giulia, Reggiani Bonetti, L., Zanocco Marani, Tommaso, Pincelli, Carlo |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6593104/ https://www.ncbi.nlm.nih.gov/pubmed/31275323 http://dx.doi.org/10.3389/fimmu.2019.01387 |
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