Reversal of life-threatening hepatopulmonary syndrome in Gaucher disease by imiglucerase enzyme replacement therapy

Advanced liver disease complicated by hepatopulmonary syndrome is a recognized complication of Gaucher disease. Macrophage-targeted, recombinant enzyme replacement therapy is effective in reversing clinical manifestations attributed to the accumulation of glycolipid-laden macrophages but it is not k...

Descripción completa

Detalles Bibliográficos
Autores principales: Beshlawy, Amal El, Murugesan, Vagishwari, Mistry, Pramod Kumar, Eid, Khaled
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2019
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6606832/
https://www.ncbi.nlm.nih.gov/pubmed/31309038
http://dx.doi.org/10.1016/j.ymgmr.2019.100490

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6606832/
https://www.ncbi.nlm.nih.gov/pubmed/31309038
http://dx.doi.org/10.1016/j.ymgmr.2019.100490

Ejemplares similares