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Solitary orbital myofibroma in a child: A rare case report with literature review

Myofibroma is a rare benign mesenchymal tumor of uncertain histogenesis. A six-year-old boy presented with a unilateral lower eyelid mass of six weeks’ duration. MRI revealed a circumscribed mass in the inferolateral orbit with bony erosion. A systemic examination was unremarkable. Excision with his...

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Autores principales: Madhuri, Bejjanki Kavya, Tripathy, Devjyoti, Mittal, Ruchi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6611317/
https://www.ncbi.nlm.nih.gov/pubmed/31238482
http://dx.doi.org/10.4103/ijo.IJO_1553_18
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author Madhuri, Bejjanki Kavya
Tripathy, Devjyoti
Mittal, Ruchi
author_facet Madhuri, Bejjanki Kavya
Tripathy, Devjyoti
Mittal, Ruchi
author_sort Madhuri, Bejjanki Kavya
collection PubMed
description Myofibroma is a rare benign mesenchymal tumor of uncertain histogenesis. A six-year-old boy presented with a unilateral lower eyelid mass of six weeks’ duration. MRI revealed a circumscribed mass in the inferolateral orbit with bony erosion. A systemic examination was unremarkable. Excision with histopathology revealed a partially infiltrative spindle cell tumor with bland nuclear morphology expressing smooth muscle actin and muscle-specific actin, compatible with myofibroma. Solitary myofibroma is a rare childhood orbital tumor and may clinico-radiologically closely mimic a malignancy. Histopathology and immunohistochemistry can help reach a definitive diagnosis. Systemic evaluation and close follow up are crucial in such cases.
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spelling pubmed-66113172019-07-22 Solitary orbital myofibroma in a child: A rare case report with literature review Madhuri, Bejjanki Kavya Tripathy, Devjyoti Mittal, Ruchi Indian J Ophthalmol Case Reports Myofibroma is a rare benign mesenchymal tumor of uncertain histogenesis. A six-year-old boy presented with a unilateral lower eyelid mass of six weeks’ duration. MRI revealed a circumscribed mass in the inferolateral orbit with bony erosion. A systemic examination was unremarkable. Excision with histopathology revealed a partially infiltrative spindle cell tumor with bland nuclear morphology expressing smooth muscle actin and muscle-specific actin, compatible with myofibroma. Solitary myofibroma is a rare childhood orbital tumor and may clinico-radiologically closely mimic a malignancy. Histopathology and immunohistochemistry can help reach a definitive diagnosis. Systemic evaluation and close follow up are crucial in such cases. Wolters Kluwer - Medknow 2019-07 /pmc/articles/PMC6611317/ /pubmed/31238482 http://dx.doi.org/10.4103/ijo.IJO_1553_18 Text en Copyright: © 2019 Indian Journal of Ophthalmology http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Reports
Madhuri, Bejjanki Kavya
Tripathy, Devjyoti
Mittal, Ruchi
Solitary orbital myofibroma in a child: A rare case report with literature review
title Solitary orbital myofibroma in a child: A rare case report with literature review
title_full Solitary orbital myofibroma in a child: A rare case report with literature review
title_fullStr Solitary orbital myofibroma in a child: A rare case report with literature review
title_full_unstemmed Solitary orbital myofibroma in a child: A rare case report with literature review
title_short Solitary orbital myofibroma in a child: A rare case report with literature review
title_sort solitary orbital myofibroma in a child: a rare case report with literature review
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6611317/
https://www.ncbi.nlm.nih.gov/pubmed/31238482
http://dx.doi.org/10.4103/ijo.IJO_1553_18
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