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An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome
Mounier-Kuhn syndrome is a rare clinical and radiologic condition. It is characterized by tracheal and bronchial dilation. Diagnosis is made by computed tomography and bronchoscopy. An 81-year-old man presenting with an acute chest pain was referred to the pulmonology department. His chest computed...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Hindawi
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6644234/ https://www.ncbi.nlm.nih.gov/pubmed/31360573 http://dx.doi.org/10.1155/2019/5359309 |
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author | Naciri, Salim Zahraoui, Rachida Soualhi, Mouna Bourkadi, Jamal-Eddine |
author_facet | Naciri, Salim Zahraoui, Rachida Soualhi, Mouna Bourkadi, Jamal-Eddine |
author_sort | Naciri, Salim |
collection | PubMed |
description | Mounier-Kuhn syndrome is a rare clinical and radiologic condition. It is characterized by tracheal and bronchial dilation. Diagnosis is made by computed tomography and bronchoscopy. An 81-year-old man presenting with an acute chest pain was referred to the pulmonology department. His chest computed tomographic scan showed a tracheobronchomegaly with an increase in the diameter of both the trachea and right and left main bronchi, associated with pneumomediastinum and fibrosis. Fiberoptic bronchoscopy revealed enlarged trachea and both main bronchi. These findings are consistent with a diagnosis of Mounier-Kuhn syndrome. Besides considering this long-neglected “orphan disease” when diagnosing spontaneous pneumomediastinum, clinicians should also be aware of an underlying Mounier-Kuhn syndrome in patients with recurrent respiratory infections, in order to avoid complications associated with the disease. |
format | Online Article Text |
id | pubmed-6644234 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2019 |
publisher | Hindawi |
record_format | MEDLINE/PubMed |
spelling | pubmed-66442342019-07-29 An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome Naciri, Salim Zahraoui, Rachida Soualhi, Mouna Bourkadi, Jamal-Eddine Case Rep Pulmonol Case Report Mounier-Kuhn syndrome is a rare clinical and radiologic condition. It is characterized by tracheal and bronchial dilation. Diagnosis is made by computed tomography and bronchoscopy. An 81-year-old man presenting with an acute chest pain was referred to the pulmonology department. His chest computed tomographic scan showed a tracheobronchomegaly with an increase in the diameter of both the trachea and right and left main bronchi, associated with pneumomediastinum and fibrosis. Fiberoptic bronchoscopy revealed enlarged trachea and both main bronchi. These findings are consistent with a diagnosis of Mounier-Kuhn syndrome. Besides considering this long-neglected “orphan disease” when diagnosing spontaneous pneumomediastinum, clinicians should also be aware of an underlying Mounier-Kuhn syndrome in patients with recurrent respiratory infections, in order to avoid complications associated with the disease. Hindawi 2019-07-08 /pmc/articles/PMC6644234/ /pubmed/31360573 http://dx.doi.org/10.1155/2019/5359309 Text en Copyright © 2019 Salim Naciri et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Naciri, Salim Zahraoui, Rachida Soualhi, Mouna Bourkadi, Jamal-Eddine An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
title | An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
title_full | An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
title_fullStr | An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
title_full_unstemmed | An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
title_short | An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
title_sort | unusual cause of spontaneous pneumomediastinum: the mounier-kuhn syndrome |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6644234/ https://www.ncbi.nlm.nih.gov/pubmed/31360573 http://dx.doi.org/10.1155/2019/5359309 |
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