A Successful Steroid-Sparing Approach in Cronkhite-Canada Syndrome

Cronkhite-Canada Syndrome (CCS) is a rare, sporadic polyposis condition. The literature on CCS consists mostly of case reports. Although disease presentation has been well-described, there is no consensus on the management of CCS. We present a severe case of CCS that demonstrated clinical and endosc...

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Autores principales: Mao, Eric J., Hyder, Sarah M., DeNucci, Thomas D., Fine, Sean
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer 2019
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6658025/
https://www.ncbi.nlm.nih.gov/pubmed/31620498
http://dx.doi.org/10.14309/crj.0000000000000055
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author Mao, Eric J.
Hyder, Sarah M.
DeNucci, Thomas D.
Fine, Sean
author_facet Mao, Eric J.
Hyder, Sarah M.
DeNucci, Thomas D.
Fine, Sean
author_sort Mao, Eric J.
collection PubMed
description Cronkhite-Canada Syndrome (CCS) is a rare, sporadic polyposis condition. The literature on CCS consists mostly of case reports. Although disease presentation has been well-described, there is no consensus on the management of CCS. We present a severe case of CCS that demonstrated clinical and endoscopic response to corticosteroids. This response was maintained with azathioprine. This case provides additional experience on a therapeutic strategy to induce and maintain a durable corticosteroid-free remission.
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spelling pubmed-66580252019-10-16 A Successful Steroid-Sparing Approach in Cronkhite-Canada Syndrome Mao, Eric J. Hyder, Sarah M. DeNucci, Thomas D. Fine, Sean ACG Case Rep J Case Report Cronkhite-Canada Syndrome (CCS) is a rare, sporadic polyposis condition. The literature on CCS consists mostly of case reports. Although disease presentation has been well-described, there is no consensus on the management of CCS. We present a severe case of CCS that demonstrated clinical and endoscopic response to corticosteroids. This response was maintained with azathioprine. This case provides additional experience on a therapeutic strategy to induce and maintain a durable corticosteroid-free remission. Wolters Kluwer 2019-03-27 /pmc/articles/PMC6658025/ /pubmed/31620498 http://dx.doi.org/10.14309/crj.0000000000000055 Text en © 2019 The Author(s). Published by Wolters Kluwer Health, Inc. on behalf of The American College of Gastroenterology. This is an open-access article distributed under the terms of the Creative Commons Attribution-Non Commercial-No Derivatives License 4.0 (CCBY-NC-ND) (http://creativecommons.org/licenses/by-nc-nd/4.0/) , where it is permissible to download and share the work provided it is properly cited. The work cannot be changed in any way or used commercially without permission from the journal.
spellingShingle Case Report
Mao, Eric J.
Hyder, Sarah M.
DeNucci, Thomas D.
Fine, Sean
A Successful Steroid-Sparing Approach in Cronkhite-Canada Syndrome
title A Successful Steroid-Sparing Approach in Cronkhite-Canada Syndrome
title_full A Successful Steroid-Sparing Approach in Cronkhite-Canada Syndrome
title_fullStr A Successful Steroid-Sparing Approach in Cronkhite-Canada Syndrome
title_full_unstemmed A Successful Steroid-Sparing Approach in Cronkhite-Canada Syndrome
title_short A Successful Steroid-Sparing Approach in Cronkhite-Canada Syndrome
title_sort successful steroid-sparing approach in cronkhite-canada syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6658025/
https://www.ncbi.nlm.nih.gov/pubmed/31620498
http://dx.doi.org/10.14309/crj.0000000000000055
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