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Adult Langerhans cell histiocytosis presenting as metachronous colonic polyps

Langerhans cell histiocytosis (LCH) is a rare disease characterized by proliferation of Langerhans-type cells that express CD1a, Langerin (CD207) and S100 protein. Birbeck granules are a hallmark by ultrastructural examination. LCH presents with a wide clinical spectrum, ranging from solitary lesion...

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Detalles Bibliográficos
Autores principales: Felipe-Silva, Aloísio, Assef, Mauricio Saab, Rodrigues, Rodrigo Azevedo, Pagliari, Carla
Formato: Online Artículo Texto
Lenguaje:English
Publicado: São Paulo, SP: Universidade de São Paulo, Hospital Universitário 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6671878/
https://www.ncbi.nlm.nih.gov/pubmed/31528596
http://dx.doi.org/10.4322/acr.2013.006

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