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Adult Langerhans cell histiocytosis presenting as metachronous colonic polyps
Langerhans cell histiocytosis (LCH) is a rare disease characterized by proliferation of Langerhans-type cells that express CD1a, Langerin (CD207) and S100 protein. Birbeck granules are a hallmark by ultrastructural examination. LCH presents with a wide clinical spectrum, ranging from solitary lesion...
Autores principales: | Felipe-Silva, Aloísio, Assef, Mauricio Saab, Rodrigues, Rodrigo Azevedo, Pagliari, Carla |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
São Paulo, SP: Universidade de São Paulo, Hospital Universitário
2013
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6671878/ https://www.ncbi.nlm.nih.gov/pubmed/31528596 http://dx.doi.org/10.4322/acr.2013.006 |
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