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Management of severe hypertriglyceridemia due to lipoprotein lipase deficiency in children

Severe hypertriglyceridemia is an endocrine emergency and is associated with acute pancreatitis and hyperviscosity syndrome. We describe an infant with lipoprotein lipase deficiency with severe hypertriglyceridemia who presented with acute pancreatitis. She was managed acutely with fasting and intra...

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Detalles Bibliográficos
Autores principales:	Poon, Sarah W Y, Leung, Karen K Y, Tung, Joanna Y L
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Bioscientifica Ltd 2019
Materias:	Insight into Disease Pathogenesis or Mechanism of Therapy
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6685095/ https://www.ncbi.nlm.nih.gov/pubmed/31352695 http://dx.doi.org/10.1530/EDM-19-0052

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