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NAD+ improves neuromuscular development in a zebrafish model of FKRP-associated dystroglycanopathy
BACKGROUND: Secondary dystroglycanopathies are muscular dystrophies that result from mutations in genes that participate in Dystroglycan glycosylation. Glycosylation of Dystroglycan is essential for muscle fibers to adhere to the muscle extracellular matrix (myomatrix). Although the myomatrix is dis...
Autores principales: | Bailey, Erin C., Alrowaished, Sarah S., Kilroy, Elisabeth A., Crooks, Emma S., Drinkert, Daisy M., Karunasiri, Chaya M., Belanger, Joseph J., Khalil, Andre, Kelley, Joshua B., Henry, Clarissa A. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6685180/ https://www.ncbi.nlm.nih.gov/pubmed/31391079 http://dx.doi.org/10.1186/s13395-019-0206-1 |
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