Prune belly syndrome: current perspectives

Prune belly syndrome (PBS) is a rare but morbid congenital disease, classically defined by a triad of cardinal features that includes cryptorchidism, urinary tract dilation and laxity of the abdominal wall musculature. Children often require numerous surgical interventions including bilateral orchid...

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Detalles Bibliográficos
Autores principales: Arlen, Angela M, Nawaf, Cayce, Kirsch, Andrew J
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Dove 2019
Materias:
Review
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6689549/
https://www.ncbi.nlm.nih.gov/pubmed/31496864
http://dx.doi.org/10.2147/PHMT.S188014
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author Arlen, Angela M
Nawaf, Cayce
Kirsch, Andrew J
author_facet Arlen, Angela M
Nawaf, Cayce
Kirsch, Andrew J
author_sort Arlen, Angela M
collection PubMed
description Prune belly syndrome (PBS) is a rare but morbid congenital disease, classically defined by a triad of cardinal features that includes cryptorchidism, urinary tract dilation and laxity of the abdominal wall musculature. Children often require numerous surgical interventions including bilateral orchidopexy as well as individually tailored urinary tract and abdominal wall reconstruction. Along with the classic features, patients with PBS often experience gastrointestinal, orthopedic, and cardiopulmonary comorbidities.
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spelling pubmed-66895492019-09-06 Prune belly syndrome: current perspectives Arlen, Angela M Nawaf, Cayce Kirsch, Andrew J Pediatric Health Med Ther Review Prune belly syndrome (PBS) is a rare but morbid congenital disease, classically defined by a triad of cardinal features that includes cryptorchidism, urinary tract dilation and laxity of the abdominal wall musculature. Children often require numerous surgical interventions including bilateral orchidopexy as well as individually tailored urinary tract and abdominal wall reconstruction. Along with the classic features, patients with PBS often experience gastrointestinal, orthopedic, and cardiopulmonary comorbidities. Dove 2019-08-06 /pmc/articles/PMC6689549/ /pubmed/31496864 http://dx.doi.org/10.2147/PHMT.S188014 Text en © 2019 Arlen et al. http://creativecommons.org/licenses/by-nc/3.0/ This work is published and licensed by Dove Medical Press Limited. The full terms of this license are available at https://www.dovepress.com/terms.php and incorporate the Creative Commons Attribution – Non Commercial (unported, v3.0) License (http://creativecommons.org/licenses/by-nc/3.0/). By accessing the work you hereby accept the Terms. Non-commercial uses of the work are permitted without any further permission from Dove Medical Press Limited, provided the work is properly attributed. For permission for commercial use of this work, please see paragraphs 4.2 and 5 of our Terms (https://www.dovepress.com/terms.php).
spellingShingle Review
Arlen, Angela M
Nawaf, Cayce
Kirsch, Andrew J
Prune belly syndrome: current perspectives
title Prune belly syndrome: current perspectives
title_full Prune belly syndrome: current perspectives
title_fullStr Prune belly syndrome: current perspectives
title_full_unstemmed Prune belly syndrome: current perspectives
title_short Prune belly syndrome: current perspectives
title_sort prune belly syndrome: current perspectives
topic Review
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6689549/
https://www.ncbi.nlm.nih.gov/pubmed/31496864
http://dx.doi.org/10.2147/PHMT.S188014
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