Brittle cornea syndrome: current perspectives

Brittle cornea syndrome (BCS) is a rare autosomal recessive connective tissue disorder characterised by severe corneal thinning, with the major ocular risk being spontaneous ocular perforation due to progressive stromal thinning and ectasia. It is a complex condition with limited treatment options....

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Detalles Bibliográficos
Autores principales: Walkden, Andrew, Burkitt-Wright, Emma, Au, Leon
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Dove 2019
Materias:
Review
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6698176/
https://www.ncbi.nlm.nih.gov/pubmed/31496642
http://dx.doi.org/10.2147/OPTH.S185287
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author Walkden, Andrew
Burkitt-Wright, Emma
Au, Leon
author_facet Walkden, Andrew
Burkitt-Wright, Emma
Au, Leon
author_sort Walkden, Andrew
collection PubMed
description Brittle cornea syndrome (BCS) is a rare autosomal recessive connective tissue disorder characterised by severe corneal thinning, with the major ocular risk being spontaneous ocular perforation due to progressive stromal thinning and ectasia. It is a complex condition with limited treatment options. The purpose of this review is to highlight the difficulties associated with the condition and examine the available published evidence with regards to management.
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spelling pubmed-66981762019-09-06 Brittle cornea syndrome: current perspectives Walkden, Andrew Burkitt-Wright, Emma Au, Leon Clin Ophthalmol Review Brittle cornea syndrome (BCS) is a rare autosomal recessive connective tissue disorder characterised by severe corneal thinning, with the major ocular risk being spontaneous ocular perforation due to progressive stromal thinning and ectasia. It is a complex condition with limited treatment options. The purpose of this review is to highlight the difficulties associated with the condition and examine the available published evidence with regards to management. Dove 2019-08-12 /pmc/articles/PMC6698176/ /pubmed/31496642 http://dx.doi.org/10.2147/OPTH.S185287 Text en © 2019 Walkden et al. http://creativecommons.org/licenses/by-nc/3.0/ This work is published and licensed by Dove Medical Press Limited. The full terms of this license are available at https://www.dovepress.com/terms.php and incorporate the Creative Commons Attribution – Non Commercial (unported, v3.0) License (http://creativecommons.org/licenses/by-nc/3.0/). By accessing the work you hereby accept the Terms. Non-commercial uses of the work are permitted without any further permission from Dove Medical Press Limited, provided the work is properly attributed. For permission for commercial use of this work, please see paragraphs 4.2 and 5 of our Terms (https://www.dovepress.com/terms.php).
spellingShingle Review
Walkden, Andrew
Burkitt-Wright, Emma
Au, Leon
Brittle cornea syndrome: current perspectives
title Brittle cornea syndrome: current perspectives
title_full Brittle cornea syndrome: current perspectives
title_fullStr Brittle cornea syndrome: current perspectives
title_full_unstemmed Brittle cornea syndrome: current perspectives
title_short Brittle cornea syndrome: current perspectives
title_sort brittle cornea syndrome: current perspectives
topic Review
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6698176/
https://www.ncbi.nlm.nih.gov/pubmed/31496642
http://dx.doi.org/10.2147/OPTH.S185287
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