Cargando…

A teenage patient with autosomal recessive polycystic kidney disease, a splenorenal shunt, and congenital hepatic fibrosis: a case report

A 16-year-old female patient previously diagnosed with autosomal recessive polycystic kidney disease (ARPKD) presented with acute bilateral pneumonia, upper gastrointestinal bleeding caused by ruptured esophageal varices, ascites, and lower limb edema. She required intensive care and an endoscopic p...

Descripción completa

Detalles Bibliográficos
Autores principales:	Scarioti, Vinicius Danieli, de Oliveira, Lucia Tabim, Mattiello, Anye Caroline, Gomes, Nayara dos Santos
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Sociedade Brasileira de Nefrologia 2018
Materias:	Case Reports
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6699426/ https://www.ncbi.nlm.nih.gov/pubmed/30199558 http://dx.doi.org/10.1590/2175-8239-JBN-2018-0081

Ejemplares similares

Congenital Splenorenal Shunt with Characteristic Ultrasonographic Findings
por: Kitagawa, Sho, et al.
Publicado: (2019)

Evidence for a “Pathogenic Triumvirate” in Congenital Hepatic Fibrosis in Autosomal Recessive Polycystic Kidney Disease
por: Jiang, Lu, et al.
Publicado: (2016)

The Role of the Distal Splenorenal Shunt in the Sclerotherapy Era?
por: Henderson, J. Michael
Publicado: (1994)

A case of venous aneurysm of a splenorenal shunt
por: Yonezawa, Hiroki, et al.
Publicado: (2021)

Autosomal Recessive Polycystic Kidney Disease
por: Salati, Sajad Ahmad
Publicado: (2014)

Autosomal Recessive Polycystic Kidney Disease
por: Hafer, Ashley S., et al.
Publicado: (2017)

Should the Distal Splenorenal Shunt be Combined with Gastric Disconection and Transection?
por: Henderson, J. Michael
Publicado: (1997)

Pre-Liver Transplant: Tips Versus Distal Splenorenal Shunt
por: Faust, Thomas W., et al.
Publicado: (1997)

Portal hypertension: A critical appraisal of shunt procedures with emphasis on distal splenorenal shunt in children
por: Sharma, Nitin, et al.
Publicado: (2014)

Unconventional shunt surgery for non-cirrhotic portal hypertension in patients not suitable for proximal splenorenal shunt
por: S L, Harilal, et al.
Publicado: (2023)

A case of a spontaneous splenorenal shunt associated with the nutcracker syndrome
por: Dołowy, Joanna, et al.
Publicado: (2011)

Distal pancreatectomy with splenorenal shunt to preserve spleen in a cirrhotic patient
por: Ettorre, Giuseppe Maria, et al.
Publicado: (2017)

Adult‐onset noncirrhotic hyperammonemic encephalopathy probably caused by splenorenal shunts
por: Yoshizawa, Kazuhiro, et al.
Publicado: (2022)

Transient Elastography for Detection of Liver Fibrosis in Children With Autosomal Recessive Polycystic Kidney Disease
por: Wicher, Dorota, et al.
Publicado: (2019)

Autosomal recessive polycystic kidney disease diagnosed in fetus
por: Thomas, Joseph, et al.
Publicado: (2007)

Molecular Pathophysiology of Autosomal Recessive Polycystic Kidney Disease
por: Cordido, Adrian, et al.
Publicado: (2021)

Autosomal Recessive Inheritance: Cystic Fibrosis
por: Goldstein, D. Yitzchak, et al.
Publicado: (2017)

Portal hypertension from nodular regenerative hyperplasia of the liver with distal splenorenal shunt
por: Greene, JA, et al.
Publicado: (2012)

Renoportal anastomosis in living donor liver transplantation with prior proximal splenorenal shunt
por: Ozdemir, Fatih, et al.
Publicado: (2017)

Early clinical management of autosomal recessive polycystic kidney disease
por: Liebau, Max Christoph
Publicado: (2021)

Phenotypic Variability in Siblings With Autosomal Recessive Polycystic Kidney Disease
por: Ajiri, Ramona, et al.
Publicado: (2022)

Portal hypertension from nodular regenerative hyperplasia of the liver treated with distal splenorenal shunt
por: Greene, JA, et al.
Publicado: (2013)

Influence of spontaneous splenorenal shunts on clinical outcomes in decompensated cirrhosis and after liver transplantation
por: Saks, Karen, et al.
Publicado: (2018)

Proximal Splenorenal Shunt in a Rare Renal Vein Anomaly: A Case Report
por: Biju, Pottakkat, et al.
Publicado: (2019)

Proximal Splenorenal Shunt Surgery for Bleeding Gastric Varices in Non-Cirrhotic Portal Hypertension
por: Anand, Utpal, et al.
Publicado: (2020)

Fatal outcome of autosomal recessive polycystic kidney disease in neonates with recessive PKHD1 mutations
por: Jung, Jiwon, et al.
Publicado: (2020)

Surgical management of extrahepatic portal vein obstruction in children: advantages of MesoRex shunt compared with distal splenorenal shunt
por: Khamag, Omar, et al.
Publicado: (2023)

Autosomal dominant and autosomal recessive polycystic kidney disease: hypertension and secondary cardiovascular effect in children
por: Lucchetti, L., et al.
Publicado: (2023)

Autosomal Recessive Polycystic Kidney Disease: Antenatal Diagnosis and Histopathological Correlation
por: Rajanna, Dayananda Kumar, et al.
Publicado: (2013)

Genetics of Autosomal Recessive Polycystic Kidney Disease and Its Differential Diagnoses
por: Bergmann, Carsten
Publicado: (2018)

Extracranial Aneurysms in 2 Patients with Autosomal Recessive Polycystic Kidney Disease
por: Elchediak, Daniel S., et al.
Publicado: (2017)

Diagnosis and Management of Hepatobiliary Complications in Autosomal Recessive Polycystic Kidney Disease
por: Wehrman, Andrew, et al.
Publicado: (2017)

Clinical and genetic characteristics of autosomal recessive polycystic kidney disease in Oman
por: Al Alawi, Intisar, et al.
Publicado: (2020)

Multiple Cerebral Aneurysms in an Adult With Autosomal Recessive Polycystic Kidney Disease
por: Gately, Ryan, et al.
Publicado: (2020)

Therapeutic Potential for CFTR Correctors in Autosomal Recessive Polycystic Kidney Disease
por: Yanda, Murali K., et al.
Publicado: (2021)

De novo mutations in autosomal recessive congenital malformations
por: Black, Holly A., et al.
Publicado: (2016)

Unusual bleeding from hepaticojejunostomy controlled by side-to-side splenorenal shunt: A case report
por: Li, Meisheng, et al.
Publicado: (2018)

Tesevatinib ameliorates progression of polycystic kidney disease in rodent models of autosomal recessive polycystic kidney disease
por: Sweeney, William E, et al.
Publicado: (2017)

Intragenic duplication in the PHKD1 gene in autosomal recessive polycystic kidney disease
por: Miyazaki, Jun, et al.
Publicado: (2015)

Risk Factors for Neurocognitive Functioning in Children with Autosomal Recessive Polycystic Kidney Disease
por: Hooper, Stephen R.
Publicado: (2017)

Cannot write session to /tmp/vufind_sessions/sess_ep5fp8b8bi098nvcv4qksarlfb