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PAPA and FMF in two siblings: possible amplification of clinical presentation? A case report

BACKGROUND: Familial Mediterranean Fever is a monogenic autoinflammatory disease, typically characterized by recurrent attacks of fever, serositis, aphthous of oral mucosa, erythema. “Pyogenic arthritis, pyoderma gangrenosum and acne syndrome” is a rare autoinflammatory disease with variable express...

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Detalles Bibliográficos
Autores principales: Maggio, Maria Cristina, Ceccherini, Isabella, Grossi, Alice, Gattorno, Marco, Corsello, Giovanni
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6708240/
https://www.ncbi.nlm.nih.gov/pubmed/31443670
http://dx.doi.org/10.1186/s13052-019-0705-z

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