Primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland

Primitive neuroectodermal tumors (PNET) are very rare tumors that belong to a family of malignant neoplasms of tiny round cells which are derived from the neural crest. This report discusses a rare case of an adult woman with esophageal PNET, confirmed by immunohistochemistry, that presented with me...

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Autores principales: Blas Jhon, Leonardo, Sánchez-Fayos, Paloma, Martín Relloso, Maria Jesus, Calero Barón, Daniel, Porres Cubero, Juan Carlos
Formato: Online Artículo Texto
Lenguaje:English
Publicado: © Georg Thieme Verlag KG 2019
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6715439/
https://www.ncbi.nlm.nih.gov/pubmed/31475235
http://dx.doi.org/10.1055/a-0977-2614
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author Blas Jhon, Leonardo
Sánchez-Fayos, Paloma
Martín Relloso, Maria Jesus
Calero Barón, Daniel
Porres Cubero, Juan Carlos
author_facet Blas Jhon, Leonardo
Sánchez-Fayos, Paloma
Martín Relloso, Maria Jesus
Calero Barón, Daniel
Porres Cubero, Juan Carlos
author_sort Blas Jhon, Leonardo
collection PubMed
description Primitive neuroectodermal tumors (PNET) are very rare tumors that belong to a family of malignant neoplasms of tiny round cells which are derived from the neural crest. This report discusses a rare case of an adult woman with esophageal PNET, confirmed by immunohistochemistry, that presented with metastasis to the pineal gland. To our knowledge, this is the first case report of a PNET with these features. Despite surgery and chemotherapeutic treatment, our case has shown disease progression.
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spelling pubmed-67154392019-09-01 Primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland Blas Jhon, Leonardo Sánchez-Fayos, Paloma Martín Relloso, Maria Jesus Calero Barón, Daniel Porres Cubero, Juan Carlos Endosc Int Open Primitive neuroectodermal tumors (PNET) are very rare tumors that belong to a family of malignant neoplasms of tiny round cells which are derived from the neural crest. This report discusses a rare case of an adult woman with esophageal PNET, confirmed by immunohistochemistry, that presented with metastasis to the pineal gland. To our knowledge, this is the first case report of a PNET with these features. Despite surgery and chemotherapeutic treatment, our case has shown disease progression. © Georg Thieme Verlag KG 2019-09 2019-08-29 /pmc/articles/PMC6715439/ /pubmed/31475235 http://dx.doi.org/10.1055/a-0977-2614 Text en https://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial-NoDerivatives License, which permits unrestricted reproduction and distribution, for non-commercial purposes only; and use and reproduction, but not distribution, of adapted material for non-commercial purposes only, provided the original work is properly cited.
spellingShingle Blas Jhon, Leonardo
Sánchez-Fayos, Paloma
Martín Relloso, Maria Jesus
Calero Barón, Daniel
Porres Cubero, Juan Carlos
Primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland
title Primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland
title_full Primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland
title_fullStr Primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland
title_full_unstemmed Primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland
title_short Primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland
title_sort primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6715439/
https://www.ncbi.nlm.nih.gov/pubmed/31475235
http://dx.doi.org/10.1055/a-0977-2614
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