First report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond Fontan

We report a case of hypoplastic left heart syndrome with an anomalous left coronary artery from the pulmonary artery (ALCAPA) identified intraoperatively during the Stage-II palliation. Due to recurring ventricular fibrillation on sternotomy, a hybrid Stage-I palliation was performed. During compreh...

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Autores principales: Riggs, Kyle W, Price, Nina M, Szugye, Nicholas, Goldstein, Bryan H, Morales, David L S
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2019
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6716304/
https://www.ncbi.nlm.nih.gov/pubmed/31516293
http://dx.doi.org/10.4103/apc.APC_152_18
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author Riggs, Kyle W
Price, Nina M
Szugye, Nicholas
Goldstein, Bryan H
Morales, David L S
author_facet Riggs, Kyle W
Price, Nina M
Szugye, Nicholas
Goldstein, Bryan H
Morales, David L S
author_sort Riggs, Kyle W
collection PubMed
description We report a case of hypoplastic left heart syndrome with an anomalous left coronary artery from the pulmonary artery (ALCAPA) identified intraoperatively during the Stage-II palliation. Due to recurring ventricular fibrillation on sternotomy, a hybrid Stage-I palliation was performed. During comprehensive Stage-II, the ALCAPA was reimplanted in the neoaorta and measures, including a nontraditional Damus connection/arch reconstruction and classic bilateral Glenn procedures, were taken to avoid compression of the coronary artery. After a successful Fontan procedure, he continues to do well at 5 years old, becoming the first patient reported in the literature to survive all the three stages of single-ventricle palliation.
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spelling pubmed-67163042019-09-12 First report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond Fontan Riggs, Kyle W Price, Nina M Szugye, Nicholas Goldstein, Bryan H Morales, David L S Ann Pediatr Cardiol Case Report We report a case of hypoplastic left heart syndrome with an anomalous left coronary artery from the pulmonary artery (ALCAPA) identified intraoperatively during the Stage-II palliation. Due to recurring ventricular fibrillation on sternotomy, a hybrid Stage-I palliation was performed. During comprehensive Stage-II, the ALCAPA was reimplanted in the neoaorta and measures, including a nontraditional Damus connection/arch reconstruction and classic bilateral Glenn procedures, were taken to avoid compression of the coronary artery. After a successful Fontan procedure, he continues to do well at 5 years old, becoming the first patient reported in the literature to survive all the three stages of single-ventricle palliation. Wolters Kluwer - Medknow 2019 /pmc/articles/PMC6716304/ /pubmed/31516293 http://dx.doi.org/10.4103/apc.APC_152_18 Text en Copyright: © 2019 Annals of Pediatric Cardiology http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Riggs, Kyle W
Price, Nina M
Szugye, Nicholas
Goldstein, Bryan H
Morales, David L S
First report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond Fontan
title First report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond Fontan
title_full First report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond Fontan
title_fullStr First report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond Fontan
title_full_unstemmed First report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond Fontan
title_short First report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond Fontan
title_sort first report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond fontan
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6716304/
https://www.ncbi.nlm.nih.gov/pubmed/31516293
http://dx.doi.org/10.4103/apc.APC_152_18
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