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Anomalous aortic origin of the pulmonary arteries: Case series and literature review
Anomalous origin of the pulmonary arteries from the ascending aorta is a rare, but severe clinical entity necessitating a scrupulous evaluation. Either the right or the left pulmonary arteries can arise directly from the ascending aorta while the other pulmonary artery retains its origin from the ri...
Autores principales: | , , , , , , , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Wolters Kluwer - Medknow
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6716331/ https://www.ncbi.nlm.nih.gov/pubmed/31516282 http://dx.doi.org/10.4103/apc.APC_89_18 |
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author | Agati, Salvatore Sousa, Carlos Guerra Calvaruso, Felice Davide Zanai, Rosanna Campanella, Ivana Poli, Daniela Di Pino, Alfredo Borro, Luca Iorio, Fiore Salvatore Raponi, Massimiliano Anderson, Robert H Reali, Simone De Zorzi, Andrea Secinaro, Aurelio |
author_facet | Agati, Salvatore Sousa, Carlos Guerra Calvaruso, Felice Davide Zanai, Rosanna Campanella, Ivana Poli, Daniela Di Pino, Alfredo Borro, Luca Iorio, Fiore Salvatore Raponi, Massimiliano Anderson, Robert H Reali, Simone De Zorzi, Andrea Secinaro, Aurelio |
author_sort | Agati, Salvatore |
collection | PubMed |
description | Anomalous origin of the pulmonary arteries from the ascending aorta is a rare, but severe clinical entity necessitating a scrupulous evaluation. Either the right or the left pulmonary arteries can arise directly from the ascending aorta while the other pulmonary artery retains its origin from the right ventricular outflow tract. Such a finding can be isolated or can coexist with several congenital heart lesions. Direct intrapericardial aortic origin, however, must be distinguished with origin through a persistently patent arterial duct. In the current era, clinical manifestations usually become evident in the newborn rather than during infancy, as used to be the case. They include respiratory distress or congestive heart failure due to increased pulmonary flow and poor feeding. The rate of survival has now increased due to early diagnosis and prompt surgical repair, should now be expected to be at least 95%. We have treated four neonates with this lesion over the past 7 years, all of whom survived surgical repair. Right ventricular systolic pressure was significantly decreased at follow-up. Our choice of treatment was to translocate the anomalous pulmonary artery in end-to-side fashion to the pulmonary trunk. Our aim in this report is to update an Italian experience in the diagnosis and treatment of anomalous direct origin of one pulmonary artery from the aorta, adding considerations on the lessons learned from our most recent review of the salient literature. |
format | Online Article Text |
id | pubmed-6716331 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2019 |
publisher | Wolters Kluwer - Medknow |
record_format | MEDLINE/PubMed |
spelling | pubmed-67163312019-09-12 Anomalous aortic origin of the pulmonary arteries: Case series and literature review Agati, Salvatore Sousa, Carlos Guerra Calvaruso, Felice Davide Zanai, Rosanna Campanella, Ivana Poli, Daniela Di Pino, Alfredo Borro, Luca Iorio, Fiore Salvatore Raponi, Massimiliano Anderson, Robert H Reali, Simone De Zorzi, Andrea Secinaro, Aurelio Ann Pediatr Cardiol State of the Art Anomalous origin of the pulmonary arteries from the ascending aorta is a rare, but severe clinical entity necessitating a scrupulous evaluation. Either the right or the left pulmonary arteries can arise directly from the ascending aorta while the other pulmonary artery retains its origin from the right ventricular outflow tract. Such a finding can be isolated or can coexist with several congenital heart lesions. Direct intrapericardial aortic origin, however, must be distinguished with origin through a persistently patent arterial duct. In the current era, clinical manifestations usually become evident in the newborn rather than during infancy, as used to be the case. They include respiratory distress or congestive heart failure due to increased pulmonary flow and poor feeding. The rate of survival has now increased due to early diagnosis and prompt surgical repair, should now be expected to be at least 95%. We have treated four neonates with this lesion over the past 7 years, all of whom survived surgical repair. Right ventricular systolic pressure was significantly decreased at follow-up. Our choice of treatment was to translocate the anomalous pulmonary artery in end-to-side fashion to the pulmonary trunk. Our aim in this report is to update an Italian experience in the diagnosis and treatment of anomalous direct origin of one pulmonary artery from the aorta, adding considerations on the lessons learned from our most recent review of the salient literature. Wolters Kluwer - Medknow 2019 /pmc/articles/PMC6716331/ /pubmed/31516282 http://dx.doi.org/10.4103/apc.APC_89_18 Text en Copyright: © 2019 Annals of Pediatric Cardiology http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms. |
spellingShingle | State of the Art Agati, Salvatore Sousa, Carlos Guerra Calvaruso, Felice Davide Zanai, Rosanna Campanella, Ivana Poli, Daniela Di Pino, Alfredo Borro, Luca Iorio, Fiore Salvatore Raponi, Massimiliano Anderson, Robert H Reali, Simone De Zorzi, Andrea Secinaro, Aurelio Anomalous aortic origin of the pulmonary arteries: Case series and literature review |
title | Anomalous aortic origin of the pulmonary arteries: Case series and literature review |
title_full | Anomalous aortic origin of the pulmonary arteries: Case series and literature review |
title_fullStr | Anomalous aortic origin of the pulmonary arteries: Case series and literature review |
title_full_unstemmed | Anomalous aortic origin of the pulmonary arteries: Case series and literature review |
title_short | Anomalous aortic origin of the pulmonary arteries: Case series and literature review |
title_sort | anomalous aortic origin of the pulmonary arteries: case series and literature review |
topic | State of the Art |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6716331/ https://www.ncbi.nlm.nih.gov/pubmed/31516282 http://dx.doi.org/10.4103/apc.APC_89_18 |
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