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Pleomorphic Pulmonary Manifestations of IgG4-Related Disease

Immunoglobulin G4-related disease (IgG4-RD) is a fibroinflammatory disorder which has been first reported in 2001 by Hamano and colleagues in a patient with autoimmune sclerosing pancreatitis. Almost every organ in the human body can be affected by IgG4-RD from infiltration with IgG4-positive plasma...

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Autores principales: Naramala, Srikanth, Biswas, Sharmi, Adapa, Sreedhar, Gayam, Vijay, Castillo, Romeo C., Annangi, Srinadh, Konala, Venu Madhav
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6721390/
https://www.ncbi.nlm.nih.gov/pubmed/31531258
http://dx.doi.org/10.1155/2019/7572869
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author Naramala, Srikanth
Biswas, Sharmi
Adapa, Sreedhar
Gayam, Vijay
Castillo, Romeo C.
Annangi, Srinadh
Konala, Venu Madhav
author_facet Naramala, Srikanth
Biswas, Sharmi
Adapa, Sreedhar
Gayam, Vijay
Castillo, Romeo C.
Annangi, Srinadh
Konala, Venu Madhav
author_sort Naramala, Srikanth
collection PubMed
description Immunoglobulin G4-related disease (IgG4-RD) is a fibroinflammatory disorder which has been first reported in 2001 by Hamano and colleagues in a patient with autoimmune sclerosing pancreatitis. Almost every organ in the human body can be affected by IgG4-RD from infiltration with IgG4-positive plasma cells. Involvement of lungs with IgG4 is reported previously, but still, there is no clear picture of the pathophysiology behind lung involvement. Here, we are presenting a patient who has IgG4-RD presenting as pseudotumor of the lungs.
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spelling pubmed-67213902019-09-17 Pleomorphic Pulmonary Manifestations of IgG4-Related Disease Naramala, Srikanth Biswas, Sharmi Adapa, Sreedhar Gayam, Vijay Castillo, Romeo C. Annangi, Srinadh Konala, Venu Madhav Case Rep Rheumatol Case Report Immunoglobulin G4-related disease (IgG4-RD) is a fibroinflammatory disorder which has been first reported in 2001 by Hamano and colleagues in a patient with autoimmune sclerosing pancreatitis. Almost every organ in the human body can be affected by IgG4-RD from infiltration with IgG4-positive plasma cells. Involvement of lungs with IgG4 is reported previously, but still, there is no clear picture of the pathophysiology behind lung involvement. Here, we are presenting a patient who has IgG4-RD presenting as pseudotumor of the lungs. Hindawi 2019-08-20 /pmc/articles/PMC6721390/ /pubmed/31531258 http://dx.doi.org/10.1155/2019/7572869 Text en Copyright © 2019 Srikanth Naramala et al. http://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Naramala, Srikanth
Biswas, Sharmi
Adapa, Sreedhar
Gayam, Vijay
Castillo, Romeo C.
Annangi, Srinadh
Konala, Venu Madhav
Pleomorphic Pulmonary Manifestations of IgG4-Related Disease
title Pleomorphic Pulmonary Manifestations of IgG4-Related Disease
title_full Pleomorphic Pulmonary Manifestations of IgG4-Related Disease
title_fullStr Pleomorphic Pulmonary Manifestations of IgG4-Related Disease
title_full_unstemmed Pleomorphic Pulmonary Manifestations of IgG4-Related Disease
title_short Pleomorphic Pulmonary Manifestations of IgG4-Related Disease
title_sort pleomorphic pulmonary manifestations of igg4-related disease
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6721390/
https://www.ncbi.nlm.nih.gov/pubmed/31531258
http://dx.doi.org/10.1155/2019/7572869
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