Siblings Diagnosed With Primary Neuroendocrine Tumor of the Left Hepatic Duct

Primary left hepatic duct neuroendocrine tumors are extremely rare. We describe 2 cases of siblings, a 51-year-old brother and a 48-year-old sister, who were both diagnosed with primary left hepatic duct neuroendocrine tumor. Both patients underwent successful left hepatectomy and are both alive wit...

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Detalles Bibliográficos
Autores principales: Dayan, Aviel, Ricci, Claudio, Campana, Davide, Santini, Donatella, Fughelli, Patrizia, Minni, Francesco, Nardo, Bruno
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer 2019
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6722381/
https://www.ncbi.nlm.nih.gov/pubmed/31620513
http://dx.doi.org/10.14309/crj.0000000000000104
Descripción
Sumario:Primary left hepatic duct neuroendocrine tumors are extremely rare. We describe 2 cases of siblings, a 51-year-old brother and a 48-year-old sister, who were both diagnosed with primary left hepatic duct neuroendocrine tumor. Both patients underwent successful left hepatectomy and are both alive with no recurrence. For this rare malignancy, while definitive diagnosis is made only by histopathology, a margin-free surgical resection remains the only curative treatment modality to date.

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