Siblings Diagnosed With Primary Neuroendocrine Tumor of the Left Hepatic Duct

Primary left hepatic duct neuroendocrine tumors are extremely rare. We describe 2 cases of siblings, a 51-year-old brother and a 48-year-old sister, who were both diagnosed with primary left hepatic duct neuroendocrine tumor. Both patients underwent successful left hepatectomy and are both alive wit...

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Detalles Bibliográficos
Autores principales: Dayan, Aviel, Ricci, Claudio, Campana, Davide, Santini, Donatella, Fughelli, Patrizia, Minni, Francesco, Nardo, Bruno
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer 2019
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6722381/
https://www.ncbi.nlm.nih.gov/pubmed/31620513
http://dx.doi.org/10.14309/crj.0000000000000104
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author Dayan, Aviel
Ricci, Claudio
Campana, Davide
Santini, Donatella
Fughelli, Patrizia
Minni, Francesco
Nardo, Bruno
author_facet Dayan, Aviel
Ricci, Claudio
Campana, Davide
Santini, Donatella
Fughelli, Patrizia
Minni, Francesco
Nardo, Bruno
author_sort Dayan, Aviel
collection PubMed
description Primary left hepatic duct neuroendocrine tumors are extremely rare. We describe 2 cases of siblings, a 51-year-old brother and a 48-year-old sister, who were both diagnosed with primary left hepatic duct neuroendocrine tumor. Both patients underwent successful left hepatectomy and are both alive with no recurrence. For this rare malignancy, while definitive diagnosis is made only by histopathology, a margin-free surgical resection remains the only curative treatment modality to date.
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spelling pubmed-67223812019-10-16 Siblings Diagnosed With Primary Neuroendocrine Tumor of the Left Hepatic Duct Dayan, Aviel Ricci, Claudio Campana, Davide Santini, Donatella Fughelli, Patrizia Minni, Francesco Nardo, Bruno ACG Case Rep J Case Report Primary left hepatic duct neuroendocrine tumors are extremely rare. We describe 2 cases of siblings, a 51-year-old brother and a 48-year-old sister, who were both diagnosed with primary left hepatic duct neuroendocrine tumor. Both patients underwent successful left hepatectomy and are both alive with no recurrence. For this rare malignancy, while definitive diagnosis is made only by histopathology, a margin-free surgical resection remains the only curative treatment modality to date. Wolters Kluwer 2019-07-17 /pmc/articles/PMC6722381/ /pubmed/31620513 http://dx.doi.org/10.14309/crj.0000000000000104 Text en © 2019 The Author(s). Published by Wolters Kluwer Health, Inc. on behalf of The American College of Gastroenterology. This is an open-accessarticle distributed under the terms of the Creative Commons Attribution-Non Commercial-No Derivatives License 4.0 (CCBY-NC-ND) (http://creativecommons.org/licenses/by-nc-nd/4.0/) , where it is permissible to download and share the work provided it is properly cited. The work cannot be changed in any way or used commercially without permission from the journal.
spellingShingle Case Report
Dayan, Aviel
Ricci, Claudio
Campana, Davide
Santini, Donatella
Fughelli, Patrizia
Minni, Francesco
Nardo, Bruno
Siblings Diagnosed With Primary Neuroendocrine Tumor of the Left Hepatic Duct
title Siblings Diagnosed With Primary Neuroendocrine Tumor of the Left Hepatic Duct
title_full Siblings Diagnosed With Primary Neuroendocrine Tumor of the Left Hepatic Duct
title_fullStr Siblings Diagnosed With Primary Neuroendocrine Tumor of the Left Hepatic Duct
title_full_unstemmed Siblings Diagnosed With Primary Neuroendocrine Tumor of the Left Hepatic Duct
title_short Siblings Diagnosed With Primary Neuroendocrine Tumor of the Left Hepatic Duct
title_sort siblings diagnosed with primary neuroendocrine tumor of the left hepatic duct
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6722381/
https://www.ncbi.nlm.nih.gov/pubmed/31620513
http://dx.doi.org/10.14309/crj.0000000000000104
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