Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report

Conjoined twining is a rare medical phenomenon, with an overall prevalence of 1.47 per 100 000 births. This report describes a successful separation of xypho-omphalopagus conjoined twins complicated by unbalanced blood shunting through the porto-systemic anastomoses within the shared liver parenchym...

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Autores principales: Grizelj, Ruža, Sindičić Dessardo, Nada, Bulić, Krešimir, Luetić, Tomislav, Mikulić, Danko, Antabak, Anko, Sjekavica, Ivica, Alduk, Ana Marija, Konosić, Sanja, Režek Tomašić, Karolina, Ćaleta, Tomislav, Pleško, Sanja, Šarić, Dalibor, Vuković, Jurica
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Croatian Medical Schools 2019
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6734570/
https://www.ncbi.nlm.nih.gov/pubmed/31483115
http://dx.doi.org/10.3325/cmj.2019.60.301
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author Grizelj, Ruža
Sindičić Dessardo, Nada
Bulić, Krešimir
Luetić, Tomislav
Mikulić, Danko
Antabak, Anko
Sjekavica, Ivica
Alduk, Ana Marija
Konosić, Sanja
Režek Tomašić, Karolina
Ćaleta, Tomislav
Pleško, Sanja
Šarić, Dalibor
Vuković, Jurica
author_facet Grizelj, Ruža
Sindičić Dessardo, Nada
Bulić, Krešimir
Luetić, Tomislav
Mikulić, Danko
Antabak, Anko
Sjekavica, Ivica
Alduk, Ana Marija
Konosić, Sanja
Režek Tomašić, Karolina
Ćaleta, Tomislav
Pleško, Sanja
Šarić, Dalibor
Vuković, Jurica
author_sort Grizelj, Ruža
collection PubMed
description Conjoined twining is a rare medical phenomenon, with an overall prevalence of 1.47 per 100 000 births. This report describes a successful separation of xypho-omphalopagus conjoined twins complicated by unbalanced blood shunting through the porto-systemic anastomoses within the shared liver parenchyma. Significant extrauterine twin-twin transfusion syndrome caused by unbalanced shunting is an extremely rare, and probably under-recognized, hemodynamic complication in conjoined twins necessitating urgent separation. Progressive deterioration with a poor outcome can be prevented if the condition is recognized in a timely manner.
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spelling pubmed-67345702019-09-13 Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report Grizelj, Ruža Sindičić Dessardo, Nada Bulić, Krešimir Luetić, Tomislav Mikulić, Danko Antabak, Anko Sjekavica, Ivica Alduk, Ana Marija Konosić, Sanja Režek Tomašić, Karolina Ćaleta, Tomislav Pleško, Sanja Šarić, Dalibor Vuković, Jurica Croat Med J Case Report Conjoined twining is a rare medical phenomenon, with an overall prevalence of 1.47 per 100 000 births. This report describes a successful separation of xypho-omphalopagus conjoined twins complicated by unbalanced blood shunting through the porto-systemic anastomoses within the shared liver parenchyma. Significant extrauterine twin-twin transfusion syndrome caused by unbalanced shunting is an extremely rare, and probably under-recognized, hemodynamic complication in conjoined twins necessitating urgent separation. Progressive deterioration with a poor outcome can be prevented if the condition is recognized in a timely manner. Croatian Medical Schools 2019-08 /pmc/articles/PMC6734570/ /pubmed/31483115 http://dx.doi.org/10.3325/cmj.2019.60.301 Text en Copyright © 2019 by the Croatian Medical Journal. All rights reserved. http://creativecommons.org/licenses/by/2.5/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Grizelj, Ruža
Sindičić Dessardo, Nada
Bulić, Krešimir
Luetić, Tomislav
Mikulić, Danko
Antabak, Anko
Sjekavica, Ivica
Alduk, Ana Marija
Konosić, Sanja
Režek Tomašić, Karolina
Ćaleta, Tomislav
Pleško, Sanja
Šarić, Dalibor
Vuković, Jurica
Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report
title Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report
title_full Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report
title_fullStr Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report
title_full_unstemmed Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report
title_short Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report
title_sort successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6734570/
https://www.ncbi.nlm.nih.gov/pubmed/31483115
http://dx.doi.org/10.3325/cmj.2019.60.301
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